RESUMO
A case of liver transplantation for HCC complicating BA in an eight-month old infant is reported. HCC in BA is extremely rare. Screening of AFP and ultrasonographic examination should be performed regularly in patients with secondary biliary cirrhosis for early detection of HCC.
Assuntos
Atresia Biliar/complicações , Atresia Biliar/cirurgia , Carcinoma Hepatocelular/cirurgia , Neoplasias Hepáticas/cirurgia , Transplante de Fígado , Atresia Biliar/patologia , Carcinoma Hepatocelular/patologia , Humanos , Terapia de Imunossupressão/métodos , Imunossupressores/uso terapêutico , Recém-Nascido , Neoplasias Hepáticas/patologia , Transplante de Fígado/imunologia , Masculino , Resultado do Tratamento , alfa-Fetoproteínas/análiseRESUMO
Whereas physiologic jaundice constitutes a common finding in neonates, a few cases present with cholestatic jaundice owing to various pathologic conditions, including extrahepatic biliary obstruction. We report the case of a 2-day-old female neonate presenting with neonatal cholestasis, nonbilious vomiting with pyloric obstruction, and multiple intestinal atresias. A pathognomonic clinicoradiologic triad is described, based on clinical data, plain abdominal x-ray, and ultrasound examination.
