RESUMO
A case of Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum) is described. Seventeen years after the diagnosis was made, the patient developed a malignant astrocytoma of the cerebrum, an association only once previously reported. The clinical presentation and radiological features are presented.
Assuntos
Astrocitoma/complicações , Astrocitoma/patologia , Neoplasias Encefálicas/diagnóstico , Neoplasias Encefálicas/patologia , Neoplasias Cerebelares/complicações , Neoplasias Cerebelares/patologia , Cerebelo/patologia , Ganglioneuroma/complicações , Lobo Occipital/patologia , Adulto , Astrocitoma/diagnóstico , Neoplasias Encefálicas/complicações , Diabetes Mellitus Tipo 1/complicações , Feminino , Ganglioneuroma/patologia , Humanos , Imageamento por Ressonância Magnética , Tomografia Computadorizada por Raios XRESUMO
We report twenty-four patients with cirsoid aneurysms of the scalp. For nine patients (38%), the lesions were related to trauma. Each of the patients presented with a pulsatile scalp swelling with a bruit. No focal neurological deficits were noted in any of the patients. Scalp malformations in all patients were confirmed by selective internal and external carotid angiography, with no intracerebral component revealed in any of the patients. Twenty-one patients had the lesions surgically excised, with good results. The remaining three refused surgical intervention. Meticulous surgical technique, which includes removal of the pericranial component of the malformation, was paramount.
