[Urologic manifestations in Wolfram's syndrome]. / Manifestaciones urológicas en el síndrome de Wolfram.

The association of insipidus diabetes, diabetes mellitus, optic atrophy and deafness is known as the Wolfram syndrome. This paper contributes two case reports with significant urological sings and symptoms associated (ureterohydronephrosis, neurogenic bladder) both studied from a radiological and urodynamic point of view, with comments on the probable origin of the urological alternatives as well as their evolution, which was favourable after treatment with antibiotics and intermittent vesical catheterism.

[Renal hypoplasia and familial vesicoureteral reflux. A rare association]. / Hipoplasia renal y reflujo vesicoureteral familiar. Una rara asociación.

Presentation of two cases of unilateral congenital renal hypoplasia with vesicourethral reflux in two male siblings, no twins, both diagnosed at the age of 24. With no urological history, they present with a dysuria-pollakiuria syndrome which does not even allow to have a clinical suspicion of the final diagnosis. Clinical features of both cases are discussed, and the hyperplasia-reflux association, as well as the possibility of the condition having a hereditary and familial nature, are confirmed by clinical observation as well as radiological and histological data. A literature review is undertaken but published references are very scarce.

[Emphysematous pyelonephritis]. / Pielonefritis enfisematosa.

OBJECTIVES: The etiopathogenic and therapeutic aspects of emphysematous pyelonephritis, an uncommon disease entity, are discussed. METHODS/RESULTS: We describe the clinical history of a diabetic with intercurrent gas-forming infection in the form of emphysematous pyelonephritis that was successfully treated. CONCLUSIONS: This disease entity, which is almost exclusive to diabetic patients, is unique. It produces a type of organism that warrants early and aggressive treatment.

[Carpal synovitis secondary to BCG treatment]. / Sinovitis carpiana secundaria a tratamiento con BCG.

Systemic complications in the treatment of surface vesical tumours with intracavitary BCG are uncommon; but even less common are those that become evident in the osteoarticular system. Presentation of one case of granulomatous synovitis secondary to treatment with BCG, favourably resolved after specific treatment with a triple therapy, and discussion of its pathogenesis.

[Bilateral primary ureteral endometriosis]. / Endometriosis ureteral primaria bilateral.

Exposition of a new case of primary bilateral ureteral endometriosis, a very infrequent condition where early diagnosis before treatment is difficult since no other endometrial foci are found at either the uterus or ovary level or any sites. This condition has an enormous clinical significance because in a very short interval and in a silent manner can cause complete and irreversible damage to the upper urinary tract. The article explains the clinical characteristics of the disease, and discusses the diagnostic procedures available which are generally insufficient. The importance of the histological study is emphasized, and the surgical technique and its complications are described. Also, a literature review is included.

[Hypernephroma in childhood (author's transl)]. / Hipernefroma infantil.

A case of hypernephroma in a 9 years old male is presented. The palpable mass in the right hypochondrium orientated towards a solid renal mass confirmed by intravenous pyelography, ecography and angiography. The final diagnosis was clarified by the histopathological study, due to the low incidence of hypernephroma in children. Authors believe this is the second case published in this country.