RESUMO
La asociación de eritrodermia y dermatomiositis es rara. En 6 casos encontrados mediante búsqueda en PubMed, la mitad de ellos se encontraron asociados a neoplasias del tubo digestivo (estómago e hígado). Se presenta el caso una mujer de 69 años con debilidad proximal bilateral, artralgias, fotosensibilidad, eritema facial y en heliotropo de 18 meses de evolución. Un mes antes de su ingreso hospitalario presentó disfagia alta progresiva y una dermatosis universal con eritema y escama que afectó a mucosas, palmas y plantas, acompañándose de pérdida de peso de 10 kg en 6 meses. No se logró identificar neoplasia a ningún nivel a pesar de una búsqueda intencionada (AU)
The association of erythroderma and dermatomyositis is rare. In 6 reported cases found by searching Pubmed, half of them were associated with digestive tract neoplasms (stomach and liver). We report the case of a 69 years-old woman with bilateral proximal weakness, joint pain, photosensitivity, facial and heliotrope erythema lasting 18 months. One month prior to hospital admission she showed progressive dysphagia and a universal erythema and scaling that affected mucosa, palms and soles with an accom- panying weight loss of 10 kg in 6 months. No malignancy was identified at any level despite an exhaustive search (AU)
Assuntos
Humanos , Feminino , Pessoa de Meia-Idade , Dermatomiosite/diagnóstico , Dermatomiosite/tratamento farmacológico , Dermatite Esfoliativa/complicações , Dermatite Esfoliativa/tratamento farmacológico , Debilidade Muscular/complicações , Artralgia/complicações , Artralgia , Dermatomiosite/fisiopatologia , Dermatomiosite , Transtornos de Fotossensibilidade/complicações , Transtornos de Fotossensibilidade/diagnóstico , Eritema/complicações , BiópsiaRESUMO
The association of erythroderma and dermatomyositis is rare. In 6 reported cases found by searching Pubmed, half of them were associated with digestive tract neoplasms (stomach and liver). We report the case of a 69 years-old woman with bilateral proximal weakness, joint pain, photosensitivity, facial and heliotrope erythema lasting 18 months. One month prior to hospital admission she showed progressive dysphagia and a universal erythema and scaling that affected mucosa, palms and soles with an accompanying weight loss of 10 kg in 6 months. No malignancy was identified at any level despite an exhaustive search.
Assuntos
Dermatite Esfoliativa/diagnóstico , Dermatomiosite/diagnóstico , Síndromes Paraneoplásicas/diagnóstico , Idoso , Dermatite Esfoliativa/etiologia , Dermatomiosite/etiologia , Diagnóstico Diferencial , Evolução Fatal , Feminino , HumanosRESUMO
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