RESUMO
Foetal cardiology is now a recognised chapter of both paediatric cardiology and foetal medicine. We describe here our experience with antenatal diagnosis of cardiac malformations and discuss both its genetic and epidemiological issues. Our experience confirms if need be that foetal medicine requires a well organised first-level foetal evaluation.
Assuntos
Ecocardiografia/métodos , Cardiopatias Congênitas/diagnóstico por imagem , Anormalidades Múltiplas , Feminino , Humanos , Valor Preditivo dos Testes , Gravidez , Prognóstico , Reprodutibilidade dos Testes , Ultrassonografia Pré-NatalRESUMO
The late results of 115 children with tetralogy of Fallot born and corrected between 1969 and 1988 are analyzed; the patients were distributed into 3 anatomical groups: normal pulmonary annulus (group A, 49 patients) annular stenosis (group B, 56 patients) and pulmonary atresia (group C, 10 patients). The probability of survival 15 years after correction is 97 p. 100 in cumulated groups A and B and 72 p. 100 in group C (p = 0.005). The probability of reoperation ten years after correction is 4 p. 100 in cumulated groups A and B without a previous shunt, 20 p. 100 in A and B with a previous shunt (p less than 0.05) and 55 p. 100 in group C (p = 0.0004). The proportion of serious cardiac sequellae amounts to 17 p. 100 in group A, 55 p. 100 in group B and 100 p. 100 in group C (p = 0.0005). As a whole, 55 p. 100 of the adolescents operated on for tetralogy of Fallot during infancy present a residual problem of some severity.
Assuntos
Valva Pulmonar/anormalidades , Tetralogia de Fallot/cirurgia , Análise Atuarial , Adolescente , Criança , Pré-Escolar , Feminino , Seguimentos , Humanos , Lactente , Recém-Nascido , Masculino , Complicações Pós-Operatórias , Probabilidade , Valva Pulmonar/cirurgia , Insuficiência da Valva Pulmonar/etiologia , Estenose da Valva Pulmonar/cirurgia , Reoperação , Tetralogia de Fallot/mortalidadeRESUMO
Cortical, subcortical and subependymal tubers were more completely and more clearly depicted by MR than by CT and US in a 3-week-old infant. These lesions were best shown on T1-weighted images as areas of high signal intensity.
Assuntos
Encéfalo/patologia , Miocárdio/patologia , Esclerose Tuberosa/congênito , Feminino , Humanos , Recém-Nascido , Imageamento por Ressonância Magnética , Tomografia Computadorizada por Raios X , Esclerose Tuberosa/patologia , UltrassonografiaRESUMO
An aneurysm of the left pulmonary artery developed in an infant during a staphylococcal generalized infection. The successful surgical treatment required a left pneumonectomy. In this report the causes of that rare lesion and the prognosis of pneumonectomy in infancy are reviewed.
Assuntos
Aneurisma/etiologia , Artéria Pulmonar , Sepse/complicações , Infecções Estafilocócicas/complicações , Aneurisma/cirurgia , Feminino , Humanos , Lactente , Pneumonectomia , Sepse/etiologiaAssuntos
Cardiopatias Congênitas/cirurgia , Pré-Escolar , Humanos , Lactente , Recém-Nascido , PrognósticoRESUMO
106 cases of first attack of acute rheumatic fever were recorded during a decade (ending in 1974) in a Brussels pediatric clinic. 56 patients were Belgian and 50 were children of immigrants. The incidence of acute carditis was 23% among the former, 46% among the latter (P less than or equal to 0.01), and 34% among the whole group. The frequency of residual heart disease after a 3-yr antistreptococcal prophylaxis fell to 20% among the whole group. The difference in morbidity observed between Belgian children and children of immigrants calls for a prospective epidemiological study.
Assuntos
Cardiopatia Reumática/epidemiologia , Adolescente , Bélgica , Cardiomegalia/complicações , Criança , Pré-Escolar , Etnicidade , Feminino , Insuficiência Cardíaca/complicações , Sopros Cardíacos , Humanos , Masculino , Pericardite/complicações , Prednisona/uso terapêutico , Prognóstico , Febre Reumática/diagnóstico , Febre Reumática/epidemiologia , Febre Reumática/etiologiaRESUMO
The authors describe 2 cases of Kearns-Sayre Syndrome associated with conduction defects. In one case permanent pacing was performed. The progressive development of severe conduction defects warrants close follow-up.