RESUMO
The Bochdalek diaphragmatic hernia (BDH) is a common birth defect that is associated with other congenital malformations. Hepatic mesenchymal hamartoma (HMH) is the second most common benign hepatic tumor in children. The association between BDH and HMH or ectopic hepatic tissue is uncommon. We report a case of a female newborn with a left BDH that at surgery was incidentally found to have a tumor of 3.5 cm in maximum dimension with a serous muscular membrane. The histopathological study revealed vascular-mesenchymal stroma with bile ducts entrapped and peripheral normal hepatic tissue. These findings correlate with the diagnosis of hepatic mesenchymal hamartoma (HMH) in ectopic hepatic tissue. Our objective is to report a case of a rare association between HMH and BDH as well as discuss its differential diagnosis.
Assuntos
Coristoma/diagnóstico , Diafragma/patologia , Hamartoma/diagnóstico , Hérnias Diafragmáticas Congênitas , Hepatopatias/diagnóstico , Coristoma/complicações , Coristoma/congênito , Feminino , Hamartoma/complicações , Hamartoma/congênito , Hérnia Diafragmática/complicações , Hérnia Diafragmática/diagnóstico , Humanos , Recém-Nascido , Fígado , Hepatopatias/complicações , Hepatopatias/congênitoRESUMO
El histiocitoma fibroso maligno (HFM) es el sarcoma más común de los tejidos blandos en el adulto; sin embargo, su existencia en el tracto urinario es excepcional. Realizamos una extensa revisión de la bibliografía al respecto, habiendo encontrado hasta la actualidad 29 casos de HFM de la vejiga. Presentamos el caso de un HFM de la vejiga en un paciente con diagnóstico y seguimiento por carcinoma in situ. Describimos la forma de presentación, las variedades anatomopatológicas, las características inmunohistoquímicas, la clasificación, los factores pronósticos y el tratamiento del HFM de la vejiga(AU9
Malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in the adult. However, it is only very rarely found in the urinary bladder, with only 29 cases reported to date. We present a further case of MFH of the bladder occurring in a patient diagnosed with carcinoma in situ and describe the presentation, morphology, immunohistochemistry, histological grading, prognosis and treatment(AU)
Assuntos
Humanos , Masculino , Pessoa de Meia-Idade , Histiocitoma Fibroso Maligno/diagnóstico , Histiocitoma Fibroso Maligno/patologia , Carcinoma in Situ/patologia , Bexiga Urinária/patologia , Neoplasias da Bexiga Urinária/patologia , Imuno-Histoquímica/métodos , Diagnóstico Diferencial , Síndrome Coronariana Aguda/complicações , Síndrome Coronariana Aguda/patologia , Cistoscopia , Cistectomia/métodosRESUMO
Lymphomas arising in the female genital tract are extremely uncommon. Diffuse large B-cell lymphoma and follicular lymphoma are the most common types. We describe the case of an 80-year-old woman with a recurrent lesion in the vulva initially diagnosed as a lymphoma-like lesion and evolving 7 years later into a marginal zone B-cell lymphoma (lymphoplasmacytic lymphoma). Diagnosis was based on the monotypic pattern of the plasmacellular component and the clonal rearrangement of immunoglobulin heavy chain genes. No previous cases of vulvar marginal zone B-cell lymphoma arising in the context of a persistent lymphoma-like lesion have been reported. We highlight the importance of differentiating benign from malignant lymphoid infiltrates in the vulva.
