[Hereditary maculopathy in typical retinitis pigmentosa. Apropos of 40 cases]. / L'hérédité de la maculopathie dans la rétinopathie pigmentaire typique. A propos de 40 cas.

The authors have studied the hereditary mode of transmission of 40 maculopathy associated to typical pigmentary retinopathy. The genealogic tree was established for each case along with a complete exam. The three types of modes found were: 12.5% dominant autosomal, 15% recessive autosomal, 72.5% sporadic. The authors discussed the different mode of hereditary transmission in a family of three generations. They point out the difficulties of the genetic investigations and concluded that the maculopathy doesn't have a specific transmission mode in the typical retinitis pigmentosa.