Tumores broncopulmonares primarios / Primary lung tumors

: La mayoría de las neoplasias pulmonares de los niños son metástasis. Aunque los tumores broncopulmonares primarios son raros en los niños, la mayoría son malignos. Debido a la rareza de estos tumores no se suelen incluir en el diagnóstico diferencial, por lo que se retrasa el tratamiento y esto repercute directamente en el pronóstico de la enfermedad. Exponemos cinco tumores primarios de la vía aérea: uno en la tráquea, tres en bronquios y uno en parénquima pulmonar. Estudiamos la clí- nica, las pruebas diagnósticas, el tratamiento y la anatomía patológica de cada uno. Dada su rareza es difícil pensar en ellos en el diagnóstico diferencial de las masas pulmonares, pero debemos tenerlos en cuenta ante niños con síntomas respiratorios que no mejoran con tratamiento médico convencional. Un diagnóstico precoz de este tipo de tumores permite un tratamiento adecuado y ofrece un mejor pronóstico a largo plazo (AU)

Pulmonary neoplasia in children is usually due to methastatic disease because primary lung tumors are very unfrequent. Due to its´rarity they are usually not included in the differential diagnosis of lung masses, so treatment is delayed and prognosis is worsened. Herein, we show our experience in the management of five primary tumors of the lung or the airway: one tracheal, three bronchial, and another intraparenchymatous. We study the clinical behaviour, diagnostic work-up, treatment, histology, and follow-up. Despite its rarity, a diagnosis of pulmonary tumor should be considered in any child with respiratory symptoms that does not improve with standard therapy. An early and accurate diagnosis and an adequate treatment are crutial in the prognosis of these patients (AU)

[Primary lung tumors]. / Tumores broncopulmonares primarios.

Pulmonary neoplasia in children is usually due to methastatic disease because primary lung tumors are very unfrequent. Due to its' rarity they are usually not included in the differential diagnosis of lung masses, so treatment is delayed and prognosis is worsened. Herein, we show our experience in the management of five primary tumors of the lung or the airway: one tracheal, three bronchial, and another intraparenchymatous. We study the clinical behaviour, diagnostic work-up, treatment, histology, and follow-up. Despite its rarity, a diagnosis of pulmonary tumor should be considered in any child with respiratory symptoms that does not improve with standard therapy. An early and accurate diagnosis and an adequate treatment are crutial in the prognosis of these patients.