Assuntos
Desequilíbrio Ácido-Base/terapia , Anemia Hemolítica Congênita/diagnóstico , Icterícia Neonatal/diagnóstico , Erros Inatos do Metabolismo/terapia , Desequilíbrio Ácido-Base/sangue , Anemia Hemolítica Congênita/sangue , Anemia Hemolítica Congênita/terapia , Bilirrubina/sangue , Transfusão de Eritrócitos , Eritrócitos Anormais , Pai , Feminino , Hemoglobinas/análise , Humanos , Recém-Nascido , Icterícia Neonatal/terapia , Masculino , Erros Inatos do Metabolismo/sangue , MãesRESUMO
Double outlet right ventricle (DORV) is an uncommon congenital heart disease with a poor prognosis. We report a rare case of a girl with untreated DORV who survived until adolescence, but then developed infective endocarditis with florid complications and succumbed to it. Although infective endocarditis is seldom encountered in children in developed countries, a high index of suspicion is required for those with congenital heart disease. The roles of cross-sectional imaging are demonstrated, including the usefulness of magnetic resonance imaging not only in evaluating congenital heart disease, but also in detecting incidental lesions in the extracardiac structures.
Assuntos
Dupla Via de Saída do Ventrículo Direito/complicações , Endocardite/etiologia , Adolescente , Endocardite/diagnóstico , Evolução Fatal , Feminino , HumanosRESUMO
We describe a case of variant angina and acute inferior myocardial infarction in a previously well 6-year-old boy with a strong family history of ischemic heart disease.