[An unusual lesion of the mediastinum: angiomatosis or diffuse hemangioma]. / A propos d'une lésion inhabituelle du médiastin: l'angiomatose ou hémangiome diffus.

Angiomatosis are rare benign vascular lesions representing almost 4% of vascular tumours in children and adolescent. These lesions occur in soft tissue and are clinically extensive, covering large parts of the body in a continuous pattern. Limbs are classically involved. The incidence is high in childhood and adolescence. The authors report an original case of angiomatosis or diffuse haemangioma located in the anterosuperior part of the mediastinum in a 17 year old girl. The patient consulted for increasing dyspnoea starting two years earlier. At medical imaging, calcified tumoral mass measuring 60 mm situated in the anterosuperior mediastinum was objectivated. The mass did not involve bony nor chondral structure. Teratoma or thymoma was suspected. At operation the whole tumor was resected with adherent pericardium. At histological examination, the lesion showed the presence of vascular structures inside fibro muscular and fatty tissue mixed with multiple nerve sections. In the lesion, venous walls were remarkably thick and sometimes picked or surrounded by multiple micro vessels. A Hamartomatous or proliferative origin may be discussed. The multiple components supports a hamartomatous origin, especially because of the unexpected presence of nervous elements. A proliferative process trapping preexisting vascular and nervous elements may be also considered. Furthermore, the lesion may represent a diffuse mesenchymatous proliferation as suggested by the presence of adipose tissue or glomic cells. Additional studies based on cytogenetics could surely improve the understanding of this lesion.

Calcifying fibrous pseudotumor of the pleura: a rare location.

Calcifying fibrous pseudotumor is a rare lesion recently reported in the literature. We report a new case occurring in the pleura, which is an unusual location. The patient, a 38-year-old woman, had a left pleural mass revealed by chest roentgenograms. The tumor was resected by video-assisted thoracotomy. Only 26 cases have been reported in the literature to date, but only 4 cases have been reported in the pleura. The pathogenesis is discussed but remains uncertain. Tumor resection appears to be the best option and the clinical course is benign. However, the number of cases to date is insufficient to establish therapeutic recommendations.

[Unusual presentation of giant thymolipoma]. / Presentation inhabituelle d'un thymolipome geant.

Thymolipoma is a rare thymic tumor; His frequency is estimated at 2 at 9% of all thymic tumors. His diagnosis usually easy, can be difficult with an unusual radio clinic pattern, but actually get benefice from progress in radiologic investigations especially MRI. We reported a case of a 36-year old woman, admitted for a left pleuro-pneumopathy investigation. Evolution, after antibiotic treatment and pleural effusion draining, was well. However, patient developed systolic aortic murmur and a chest-X-ray cardiomegaly supposing cardiologic dysfunction. But the normality of cardiac sonography, the ascension of diaphragma and non-specific thoracic sonographic pattern, guided to thoracic MRI. This exploration demonstrated a giant thymolipoma, which was confirmed by the histologic examination of a resected mass.