RESUMO
Acroangiodermatitis (AAD), also known as pseudo-Kaposi's sarcoma, is an uncommon benign angioproliferative condition most commonly seen in the lower extremities. This condition often presents as discolored patches that progress to painful ulcerations. The list of vascular conditions associated with this diagnosis is vast. Acroangiodermatitis presents similarly to more aggressive conditions such as Kaposi's sarcoma, making histopathologic examination helpful in its diagnosis. We present two cases of AAD in the setting of chronic venous insufficiency.
Assuntos
Acrodermatite/diagnóstico , Acrodermatite/terapia , Terapia a Laser/métodos , Sarcoma de Kaposi/patologia , Escleroterapia/métodos , Úlcera Varicosa/diagnóstico , Acrodermatite/patologia , Idoso , Biópsia por Agulha , Doença Crônica , Terapia Combinada , Diagnóstico Diferencial , Progressão da Doença , Seguimentos , Humanos , Imuno-Histoquímica , Extremidade Inferior , Masculino , Doenças Raras , Sarcoma de Kaposi/diagnóstico , Sarcoma de Kaposi/terapia , Resultado do Tratamento , Úlcera Varicosa/terapia , Cicatrização/fisiologiaRESUMO
Behçet's Disease is a syndrome characterized by recurrent, painful oral aphthous ulcers, in conjunction with 2 or more systemic manifestations - a common systemic manifestation of the disease being cutaneous lesions, which often present as papules that ulcerate to form ulcerations which exhibit the same pathergy phenomenon as pyoderma gangrenosum and are thus difficult to heal. We present a case of a type 2 diabetic male with previously undiagnosed Behçet's Disease who presented to clinic with an atypical lower extremity wound. Due to the atypical nature of the patient's wound, combined with information from the patient regarding the history of the wound and other illnesses he had, the wound was biopsied and the results from the biopsy combined with clinical suspicion yielded a diagnosis of Behçet's Disease. After understanding the nature of the wound, management of the ulceration was adjusted appropriately so as to properly treat the patient with both local wound care and medical management for the disease. Patient was referred to rheumatology for further workup and long-term management of Behçet's Disease. Correct identification and treatment of the systemic disease, as well as the lower extremity ulcerations, in patients with Behçet's Disease are critical to avoid organ and limb-threatening complications. Had the diagnosis of Behçet's not been made in this case, the patient's wound would have been at increased risk of disease-related complications - ranging from non-healing ulceration leading to amputation to renal failure to loss of eyesight.
