RESUMO
Bladder exstrophy (BE) is a rare congenital anomaly caused by an embryological defect in the closure of the abdominal wall. It comprises a spectrum of defects about severity, including epispadias in the mildest form and cloacal exstrophy in the worst. Surgical correction is required to achieve urinary continence, maintain normal renal function, achieve secured abdominal wall closure, and create cosmetically and functionally satisfactory genitalia. Iliac bone osteotomy is considered essential to achieve the above goals in most patients by reducing the tension of the closed abdominal wall layers, particularly when present late in infancy. Several types of pelvic iliac bone osteotomy have been described to aid bladder and cloacal exstrophy closure. They can be grouped into posterior iliac osteotomy, anterior iliac osteotomy, oblique (also called diagonal) iliac osteotomy, and a combination of posterior and anterior iliac osteotomy. We described here the Y-pelvic osteotomy, which was developed by the Manchester Orthopaedic Group in the United Kingdom. It has the advantage of anterior and posterior osteotomies but also has less risk to the neurovascular structures, less blood loss, and ease of surgical technique. The osteotomy was named the Y-pelvic osteotomy due to the morphological shape it resembles.
RESUMO
We, herein report a rare case of retroperitoneal gastric duplication cyst in a 5-month female infant presenting with antenatal diagnosis of right renal cyst. Post-natal evaluation showed presence of retroperitoneal cyst in the region of right adrenal gland, which progressively increased in size on serial imaging. Laparoscopic resection resulted in satisfactory recovery. Intra-operative findings and histopathology confirmed diagnosis of isolated retroperitoneal gastric duplication cyst. Authors present the clinical features of this rare entity along with feasibility of successful laparoscopic excision in infantile age group.
