RESUMO
Thirteen patients with nasomaxillo-acrodysostosis are described. Some have the facial appearance of this syndrome only, although the others are more severely affected, with skull, eyes, ears, vertebrae and peripheral extremity involvement. The features of the 13 patients were studied and compared with those described in the literature as belonging to 'maxillonasal dysostosis' and 'acrodysostosis'. It seems certain that there is in fact only one syndrome, which differs only in extent of involvement.
Assuntos
Maxila/anormalidades , Osso Nasal/anormalidades , Adolescente , Adulto , Criança , Pré-Escolar , Doenças em Gêmeos , Feminino , Humanos , Lactente , Masculino , SíndromeRESUMO
The extent of the naso-maxillo-acro-dysostosis involvement differs in each case. The three cases presented in this paper all had different orthodontic and surgical treatment approaches according to the individual involvement of the nose, maxillae, mouth and other facial features.
