RESUMO
Malignant fibrous histiocytoma (MFH) was only recognized as a primary bone tumor a few years ago. Although it is much rarer than malignant fibrous histiocytoma of soft tissues, it is not extremely uncommon. It predominantly affects long bones; however, it has been reported to occur in many different sites and at any age. MFH are aggressive tumors that can appear in association with other bone lesions, and they have a poor prognosis. We present our experience with 13 cases of MFH and review the literature to describe the main characteristics of this tumor.
Assuntos
Neoplasias Ósseas/diagnóstico por imagem , Neoplasias Ósseas/patologia , Histiocitoma Fibroso Maligno/diagnóstico por imagem , Histiocitoma Fibroso Maligno/patologia , Imageamento por Ressonância Magnética , Adulto , Idoso , Feminino , Humanos , Masculino , Pessoa de Meia-Idade , RadiografiaRESUMO
El fibrohistiocitoma maligno óseo fue reconocido como tumor óseo primario hace pocos años y, aunque mucho más raro que su homónimo de partes blandas, no es excesivamente infrecuente. Aunque afecta preferentemente a huesos largos, ha sido descrito en múltiples localizaciones y a cualquier edad. Son tumores agresivos que pueden aparecer en relación con otras lesiones óseas y tienen mal pronóstico. Presentamos nuestra experiencia con 13 casos y realizamos una revisión bibliográfica que nos permita conocer mejor las principales características de este tumor
Malignant fibrous histiocytoma (MFH) was only recognized as a primary bone tumor a few years ago. Although it is much rarer than malignant fibrous histiocytoma of soft tissues, it is not extremely uncommon. It predominately affects long bones; however, it has been reported to occur in many different sites and at any age. MFH are aggressive tumors that can appear in association with other bone lesions, and they have a poor prognosis. We present our experience with 13 cases of MFH and review the literature to describe the main characteristics of this tumor
Assuntos
Humanos , Masculino , Feminino , Adulto , Pessoa de Meia-Idade , Idoso , Neoplasias Ósseas/patologia , Neoplasias Ósseas , Histiocitoma Fibroso Benigno/patologia , Histiocitoma Fibroso Benigno , Imageamento por Ressonância MagnéticaRESUMO
Tracheobronchomegaly is characterized by tracheal and main bronchial dilatation usually associated with pulmonary parenchymatous disease. It is a rare condition and less than a hundred cases have been reported so far. Two cases of tracheobronchomegaly are here reported, one of them in an asymptomatic patients who came to medical attention because of pneumothorax (a previously non reported association); the other case was in a female patient with advanced age and history of recurrent pneumonic episodes and with marked parenchymatous involvement. In both cases the diagnostic confirmation was made by CT.
