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J Assoc Physicians India ; 56: 643-4, 2008 Aug.
Artigo em Inglês | MEDLINE | ID: mdl-19051714

RESUMO

Behçet's disease (BD) is a multi-system inflammatory disorder which presents with recurrent orogenital ulceration, uveitis, and erythema nodosum. Medium vessel vasculitis of upper limb is extremely rare and it is only reported in patients with Behçet's disease on long follow up. Mean duration from diagnosis of disease to development of vasculitis is 5.8 years. We present a patient who presented with gangrene of fingers with absent radial pulse and during course of his illness he developed features of Behçet's disease. Diagnosis was established by clinical features and histopathology and patient was treated with steroids and colchicine.


Assuntos
Arteriopatias Oclusivas/diagnóstico , Síndrome de Behçet/diagnóstico , Artéria Radial/patologia , Corticosteroides/uso terapêutico , Arteriopatias Oclusivas/tratamento farmacológico , Arteriopatias Oclusivas/etiologia , Arteriopatias Oclusivas/fisiopatologia , Síndrome de Behçet/tratamento farmacológico , Síndrome de Behçet/fisiopatologia , Colchicina/uso terapêutico , Eritema Nodoso/fisiopatologia , Humanos , Inflamação , Masculino , Pessoa de Meia-Idade , Moduladores de Tubulina/uso terapêutico , Uveíte/fisiopatologia , Vasculite/fisiopatologia
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