RESUMO
An 8-year-old girl presented with a relatively asymptomatic abdominopelvic mass that was detected in the neonatal period. She harbored a presacral mass with intraspinal extension and a right posterior mediastinal mass; all were excised completely and were ganglioneuromas. The report discusses the maturation of neuroblastoma-ganglioneuromas and details the staged management of sporadic synchronous ganglioneuromas in a child, probably the first in published English literature.
Assuntos
Ganglioneuroma/patologia , Neoplasias Primárias Múltiplas/patologia , Neoplasias Pélvicas/patologia , Criança , Diagnóstico Diferencial , Feminino , Ganglioneuroblastoma/patologia , Humanos , Periodicidade , Região SacrococcígeaRESUMO
Pancreatic heterotopia is generally asymptomatic and occurs in gut-related sites. An antenatally detected subhepatic cyst was finally diagnosed to be a congenital biliary cystic dilatation (without a caudal duodenal communication) with macroscopic Heinrich Type 2 pancreatic heterotopia. The embryogenesis and pathology of the malformation are discussed.
Assuntos
Doenças Biliares/congênito , Sistema Biliar/anormalidades , Coristoma/congênito , Pâncreas , Doenças Biliares/cirurgia , Coristoma/cirurgia , Dilatação Patológica/congênito , Dilatação Patológica/cirurgia , Humanos , Lactente , Masculino , Diagnóstico Pré-NatalRESUMO
Gastrinomas are rare neuroendocrine tumours. A 9-year-old boy who initially presented with recurrent upper abdominal pain and was managed as hyperacidity syndrome was later diagnosed to have a primary, retroperitoneal, extra pancreatic gastrinoma after an asymptomatic period of 6 years is presented. At the second presentation, the contrast-enhanced CT revealed an epigastric mass and serum gastrin was grossly elevated. A complete excision of the mass was done; histopathological evaluation showed a well-differentiated neuroendocrine tumour. At a year follow up, the child is asymptomatic and the review imaging and serum gastrin levels are normal.
