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BMJ Case Rep ; 17(7)2024 Jul 03.
Artigo em Inglês | MEDLINE | ID: mdl-38960427

RESUMO

Factor X (FX) is a vitamin K-dependent enzyme, which acts as an important coagulation factor of coagulation cascade. FX deficiency is an autosomal recessive inherited disease and is often demonstrated in families with consanguity. Pregnancy in women with congenital FX deficiency has been associated with adverse fetal outcomes. We report a case of pregnancy in women with FX deficiency. The patient needed an immediate caesarean section at 38 weeks of gestation because of severe oligohydramnios and fetal distress. FX deficiency during pregnancy was effectively managed, leading to a positive outcome through the optimal utilisation of available resources.


Assuntos
Cesárea , Deficiência do Fator X , Humanos , Feminino , Gravidez , Deficiência do Fator X/diagnóstico , Deficiência do Fator X/complicações , Adulto , Oligo-Hidrâmnio , Complicações Hematológicas na Gravidez/diagnóstico , Resultado da Gravidez , Sofrimento Fetal/etiologia
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