Your browser doesn't support javascript.
loading
Mostrar: 20 | 50 | 100
Resultados 1 - 1 de 1
Filtrar
Mais filtros











Base de dados
Intervalo de ano de publicação
1.
Ann Hepatol ; 12(2): 327-31, 2013.
Artigo em Inglês | MEDLINE | ID: mdl-23396746

RESUMO

Abernethy malformation is a rare anomaly with partial or complete congenital absence of the portal vein and subsequent development of extrahepatic portocaval shunts. We present the case of a 28-year-old woman who was incidentally diagnosed with type II Abernethy malformation and multiple aneurysms during an investigation for nonspecific abdominal pain and fever. The patient had been diagnosed with Caroli's disease at the age of 10 and liver cirrhosis, portal hypertension a few years before. To the best of our knowledge, this is the first case reported with all such congenital anomalies associated together. Ultrasound, computed tomography, including three-dimensional reconstruction, and magnetic resonance imaging were performed which revealed a side-to-side shunt between the extrahepatic portal vein and the inferior vena cava, multiple aneurismal cystic dilation of the spleen artery and left renal artery, and extensive intrahepatic bile duct cysitic dilation with calculus formation. Etiology, clinical significance and management strategies with regard to these abnormalities are discussed.


Assuntos
Doença de Caroli/complicações , Achados Incidentais , Veia Porta/anormalidades , Malformações Vasculares/complicações , Veia Cava Inferior/anormalidades , Adulto , Doença de Caroli/diagnóstico , Doença de Caroli/terapia , Diagnóstico por Imagem/métodos , Feminino , Humanos , Imageamento por Ressonância Magnética , Veia Porta/fisiopatologia , Fluxo Sanguíneo Regional , Tomografia Computadorizada por Raios X , Ultrassonografia Doppler em Cores , Malformações Vasculares/diagnóstico , Malformações Vasculares/fisiopatologia , Veia Cava Inferior/fisiopatologia
SELEÇÃO DE REFERÊNCIAS
DETALHE DA PESQUISA