RESUMO
Scimitar syndrome is characterized by anomalous pulmonary venous drainage of a part or the whole of the right lung into the inferior vena cava (IVC). It is extremely uncommon in scimitar syndrome for the pulmonary veins to drain anomalously to a site other than the IVC. The following case report describes an otherwise classical scimitar syndrome with anomalous drainage of the right lung cephalad into the right atrium near its junction with the superior vena cava.
Assuntos
Veias Pulmonares/anormalidades , Síndrome de Cimitarra/diagnóstico , Veia Cava Superior/anormalidades , Procedimentos Cirúrgicos Cardíacos , Embolização Terapêutica , Feminino , Átrios do Coração/anormalidades , Humanos , Lactente , Veias Pulmonares/diagnóstico por imagem , Veias Pulmonares/fisiopatologia , Veias Pulmonares/cirurgia , Radiografia , Síndrome de Cimitarra/diagnóstico por imagem , Síndrome de Cimitarra/fisiopatologia , Síndrome de Cimitarra/terapia , Resultado do Tratamento , Veia Cava Superior/diagnóstico por imagem , Veia Cava Superior/fisiopatologia , Veia Cava Superior/cirurgiaRESUMO
Aneurysm of sinus of Valsalva is a rare cardiac lesion that may be acquired or congenital. The presentations of RSOV range from incidental detection to frank heart failure. Right sinus of Valsalva aneurysm usually ruptures into the right ventricle. If non-coronary sinus is involved, most aneurysms erode into the right atrium. The problems described with surgical repair of RSOV include--distension of the communicating chamber at initiation of cardiopulmonary bypass (CPB), limited ability to achieve cardiac arrest if RSOV is misdiagnosed as ventricular septal defect, and air entrainment in venous drainage line on opening of the aorta, if tricuspid valve is regurgitant and total CPB is not established. We report severe hypotension and overflowing of the venous reservoir at initiation of CPB in a patient having RSOV with significant tricuspid regurgitation and discuss its optimal management.
