RESUMO
Idiopathic focal foveolar hyperplasia (FFH) is a rare cause of gastric outlet obstruction in infants. We present two cases, including the first reported association with infantile hypertrophic pyloric stenosis. The diagnostic ultrasound appearance of FFH is described. Optimal treatment is surgical excision of the involved mucosa with pyloroplasty or pyloromyotomy.
Assuntos
Mucosa Gástrica/patologia , Obstrução da Saída Gástrica/etiologia , Obstrução da Saída Gástrica/cirurgia , Diagnóstico Diferencial , Feminino , Obstrução da Saída Gástrica/diagnóstico por imagem , Obstrução da Saída Gástrica/patologia , Humanos , Hiperplasia , Hipertrofia , Lactente , Masculino , Estenose Pilórica/complicações , UltrassonografiaRESUMO
OBJECTIVE: To determine whether there are two distinct types of congenital obstruction of the proximal urethra. PATIENTS AND METHODS: Three boys with a congenital bulbar urethral narrowing (Cobb's collar) were examined. Recent papers on congenital obstructive posterior urethral membrane (COPUM) were reviewed. RESULTS: The more proximal lesion is a membranous obstruction which is able to prolapse as far as the bulbar urethra, but has paramedian folds that attach along the posterior wall of the urethra to the verumontanum, and is due to persistence of an embryological attachment between the distal verumontanum and the anterior wall of the posterior urethra. The more distal narrowing is not always obstructive and is primarily a bulbar urethral membrane, is independent of the verumontanum and external sphincter, and may represent a persistence of part of the urogenital membrane. CONCLUSIONS: There are two distinct types of congenital obstruction of the proximal urethra, with the association to the verumontanum being the distinguishing feature.
Assuntos
Obstrução Uretral/congênito , Criança , Pré-Escolar , Humanos , Masculino , Membranas/patologia , Uretra/patologia , Obstrução Uretral/classificação , Obstrução Uretral/patologiaAssuntos
Articulação do Quadril/diagnóstico por imagem , Artrite/diagnóstico por imagem , Criança , Pré-Escolar , Diagnóstico Diferencial , Epifise Deslocada/diagnóstico por imagem , Hemartrose/diagnóstico por imagem , Humanos , Artropatias/complicações , Artropatias/diagnóstico por imagem , Doença de Legg-Calve-Perthes/diagnóstico por imagem , Masculino , Dor/etiologia , UltrassonografiaRESUMO
An abnormally long common bilio-pancreatic channel has been found in association with choledochal cysts and biliary strictures in childhood. It may also present with recurrent abdominal pain, vomiting, hyperamylasaemia and jaundice. This has been termed the common channel syndrome (CCS). Two cases with the CCS presenting early in childhood are reported together with a review of the literature. Open sphincteroplasty was performed in both cases with a satisfactory outcome.
