Painful plantar keratoderma and onychodystrophy in caucasian young woman. / Queratodermia plantar dolorosa y onicodistrofia en mujer joven caucásica.

Pachonychia congenita is an uncommon genodermatosis, classified among the disorders of keratinization and caused by mutation of certain keratin genes. The characteristic clinical triad is onychodystrophy, keratoderma, and plantar pain. In addition, the patients may present with epidermal cysts, steatocystomas, leukokeratosis, and deciduous teeth.

[Atypical presentation of infantile digital fibromatosis]. / Fibromatosis digital infantil de presentación atípica.

Infantile digital fibromatosis is a rare benign fibro/myofibroblastic proliferation that almost only occurs on the fingers and toes. It is characterized by bright, round, intracytoplasmic, eosinophilic inclusions. We present a case of infantile digital fibromatosis in a 6-years-old child.

Epidemiological study of periocular dermatitis in a specialised hospital department.

Contact dermatitis is frequent skin pathology and eyelids are one of the more frequent locations of this pathology. The objective of the present work was to study the population distribution of periocular dermatitis, determine the allergens which most frequently indicate positive in patch tests and in provocative use tests, and analyse the clinical relevance of the positive tests.Patients with periocular dermatitis (N=93) underwent a thorough physical examination and a patch test with standard series. According to clinical suspicions, 76 patients underwent a patch test with specific series. Finally a provocative use test was done for 36 patients with suspected products that the patients brought. The tests were classified according their relevance.The most frequently observed allergen in the patch tests (with standard and specific series) was nickel followed by mercury, and anti-glaucoma drops in the provocative use tests with patients products.Patients' sex, age, occupation, clinical status, presence of associated periocular symptoms, and presence of atopic or seborrheic dermatitis and/or rosacea did not relate with relevance.We conclude that a clinical diagnosis may not always be made with patch tests with standard and specific series due to lack of relevance. It is important to do provocative use tests with the products suspected as allergens in those cases where patch tests with standard and specific series indicated positive for more than one allergen.

Úlcera tropical / Tropical ulcer

Presentamos el caso de un varón de 8 años procedente de Guinea Ecuatorial que consultó por una úlcera en la pierna izquierda de 6 meses de evolución.Por las características clínicas y el país de origen del paciente, la lesión era compatible con una úlcera tropical. Se instauró tratamiento antibióticooral con amoxicilina y ácido clavulánico durante 2 semanas evolucionando a la curación en menos de 2 meses

A 8-year-old male coming from Equatorial Guinea who presented with an ulcer on the left leg of 6 month’s duration is reported. The clinical appearanceand his country of origin were highly suggestive of tropical ulcer. We prescribed an oral treatment with amoxiciline and clavulanic acid for 2 weeksand the ulcer health in less than 2 months

Reticulohistiocitosis congénita autoinvolutiva / Congenital self-healing reticulohistiocytosis

Presentamos una recién nacida con erosiones en flexuras, pápulas palmo-plantares y placas rosadas en la espalda sin afectación sistémica. La histologíamostraba un infiltrado histiocitario en dermis superior con epidermotropismo. La inmunohistoquímica resultó positiva para S100 y CD1a por loque se trataba de células de Langerhans. El estudio de extensión fue negativo. Las lesiones involucionaron espontáneamente en el plazo de 2 semanas,diagnosticándose de Reticulohistiocitosis congénita autoinvolutiva

A female newborn who presented erosions on folds, papules on palms and soles and red-brownish plaques on the back without involvement of internalorgans is reported. Light microscopy showed an histiocytic infiltrate in the papillary dermis with epidermotrophism. Inmunomarking with S100and CD1a was positive; therefore the histiocytes were Langerhans cells. The systemic evaluation excluded extracutaneous involvement. The cutaneouslesions resolved spontanously in two weeks so the case was diagnosed as Congenital self-healing reticulohistiocytosis

Enfermedad de Grover de distribución zosteriforme / Zosteriform Grover's dísease

Presentamos el caso de un paciente con enfermedad de Grover[1] con una distribución zosteriforme de las lesiones cutáneas, poco usual, afectando a dos dermatomas torácicos. Revisando la literatura publicada, ha sido descrito un solo caso de dermatosis acantolitica transitoria de distribución zosteriforme en una paciente mujer inmunocomprometida [2]

We describe a patient with zosteriform transient acantholytic dermatosis. The distribution corresponded to dermatomes TI- n. Reviewing the published literature we have found only case of zosteriform transient acantholytic dermatosis in a inmunocompromised woman