RESUMO
Persistent pupillary membranes (PPMs) are a common congenital anomaly seen in 95% of neonates. Extensive PPMs, occluding the visual axis and resulting in reduced visual acuity, are relatively uncommon. We describe a case of bilateral total PPM in a 36-year-old female who presented with complaints of blurred vision in both the eyes. Dense pupillary membranes obscuring the visual axis need early surgical treatment. It is essential that the lens status remains clear along the visual axis both before and after pupilloplasty.
Assuntos
Doenças da Íris/congênito , Iris/anormalidades , Procedimentos Cirúrgicos Oftalmológicos/métodos , Adulto , Feminino , Humanos , Iris/diagnóstico por imagem , Iris/cirurgia , Doenças da Íris/diagnóstico , Doenças da Íris/cirurgia , Membranas/patologia , Doenças Raras , Acuidade VisualAssuntos
Ambliopia/diagnóstico , Adolescente , Adulto , Ambliopia/epidemiologia , Criança , Pré-Escolar , Feminino , Hospitais de Ensino/estatística & dados numéricos , Humanos , Índia/epidemiologia , Masculino , Pessoa de Meia-Idade , Estudos Prospectivos , Centros de Atenção Terciária/estatística & dados numéricos , Acuidade Visual , Adulto JovemRESUMO
Lipoid proteinosis is a rare autosomal recessive genodermatosis with abnormal lipid protein complexes deposition in different parts of the body, especially in the skin and mucus membranes of the upper aerodigestive tract. Though ocular involvement in lipoid proteinosis is rare, ophthalmologists may encounter diverse ocular complications accompanying this syndrome in clinical practice. We describe a case of lipoid proteinosis involving bilateral eyelids with pathognomonic moniliform blepharosis in a 33-year-old gentleman who presented with the complaints of itching of eye lids on and off since 10 years.
