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Am J Otolaryngol ; 27(6): 409-12, 2006.
Artigo em Inglês | MEDLINE | ID: mdl-17084226

RESUMO

Wegener's granulomatosis (WG) is a rare, idiopathic, systemic vasculitis of small vessels that manifests in multiple organ systems. Otorhinolaryngic manifestations of this disease include recurrent sinusitis and relapsing polychondritis. Periocular involvement is also a well-documented location of Wegener's disease. We present the case of a 13-year-old girl with severe WG who developed multiple recurrent orbital infections. She underwent multiple incision and drainage surgeries of each orbit and multiple courses of intravenous antibiotics. The patient persistently reaccumulated purulence in her nasolacrimal duct system and was referred to an oculoplastic surgeon for evaluation of these recurrent infections. The diagnosis of dacryocystitis as a complication of WG was made. This unique case represents a patient with severe WG developing bilateral dacryocystitis requiring bilateral dacryocystorhinostomies.


Assuntos
Dacriocistite/diagnóstico por imagem , Granulomatose com Poliangiite/complicações , Doenças Orbitárias/diagnóstico por imagem , Adolescente , Dacriocistite/microbiologia , Dacriocistite/cirurgia , Feminino , Humanos , Doenças Orbitárias/microbiologia , Doenças Orbitárias/cirurgia , Recidiva , Tomografia Computadorizada por Raios X , Resultado do Tratamento
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