RESUMO
Sweet's syndrome is an acute febrile neutrophilic dermatosis with classical clinical features. Systemic manifestations in Sweet's syndrome including fever, arthralgia, myalgia and ocular involvement are common. Pulmonary involvement is a rare manifestation that has been reported previously in 34 cases and can be fatal if left untreated. We report a striking case of Sweet's syndrome with respiratory failure secondary to bilateral pulmonary interstitial infiltrates, which rapidly responded to intravenous corticosteroid therapy. This case is an important reminder of the systemic manifestations of Sweet's syndrome and highlights the value of collaboration between different medical specialities to optimise patient management and outcomes.
Assuntos
Doenças Pulmonares Intersticiais/etiologia , Insuficiência Respiratória/etiologia , Síndrome de Sweet/complicações , Idoso de 80 Anos ou mais , Humanos , MasculinoRESUMO
We present a rare case of focal facial dermal dysplasia type 4 (FFDD4) in an otherwise healthy boy infant, presenting as bilateral preauricular scarlike defects surrounded by a hair collar, resembling membranous aplasia cutis congenita. The presence of a hair collar supports the hypothesis that FFDD is caused by abnormal closure at facial embryonic fusion lines, but unlike midline scalp defects is not associated with neurological compromise. Other types of FFDD occur at different sites and can be associated with cranial dysgraphism. Awareness of this rare condition by dermatologists is imperative to enable prompt recognition and minimize diagnostic delay.
Assuntos
Displasia Ectodérmica/diagnóstico , Face/patologia , Displasias Dérmicas Faciais Focais , Humanos , Recém-Nascido , Masculino , Pele/patologiaRESUMO
Keratoacanthoma centrifugum marginatum (KCM) is a rare variant of keratoacanthoma (KA), characterised by a progressively expanding tumour with a lack of spontaneous remission and significant scarring. KCM has been reported previously in less than 50 cases worldwide. We present the case of a large solitary KCM on the right shin of a 71-year-old woman. This was treated successfully with oral acitretin for 16 months with sustained remission at 24 months. Our case provides further supporting evidence for acitretin as a useful treatment for KCM to induce remission, prevent extensive surgery and minimise destructive scarring.
