RESUMO
Pulmonary artery damage is difficult to estimate in a patient with one pulmonary artery from the aorta, and the pulmonary artery of anomalous origin is usually damaged. We describe a newborn patient with anomalous origin of the right pulmonary artery from the aorta who presented with significant lung perfusion at the anastomotic site 6 months postoperatively; the left/right perfusion ratio was 10:90 on a scintigram. The unbalanced left/right lung perfusion gradually improved over a number of years. In a newborn patient with anomalous origin of one pulmonary artery from the aorta, unbalanced lung perfusion may improve.
Assuntos
Aorta/cirurgia , Pulmão/irrigação sanguínea , Artéria Pulmonar/anormalidades , Artéria Pulmonar/cirurgia , Anastomose Cirúrgica/métodos , Angiografia/métodos , Aorta/patologia , Feminino , Humanos , Recém-Nascido , Pulmão/diagnóstico por imagem , Período Pós-Operatório , Artéria Pulmonar/patologia , Radiografia Torácica/métodos , Cintilografia/métodos , Resultado do TratamentoRESUMO
Absent pulmonary valve with an intact ventricular septum is a rare malformation. We report a case of absent pulmonary valve and intact ventricular septum with functional near-tricuspid atresia caused by pulmonary regurgitation. Initial palliation with main pulmonary artery ligation and bilateral pulmonary artery banding was performed at 1 day of age. More antegrade flow across the tricuspid valve was recognised postoperatively, resulting in a successful right ventricular outflow tract reconstruction by a hand-sewn bileaflet polytetrafluoroethylene valve and modified Blalock-Taussig shunt at 11 days of age.
