1.
J Craniomaxillofac Surg
; 38(7): 534-7, 2010 Oct.
Artigo
em Inglês
| MEDLINE
| ID: mdl-20346687
RESUMO
Xeroderma pigmentosa (XP) is a condition inherited as an autosomal recessive trait and is characterized by photosensitivity, pigmentary changes, premature skin ageing and malignant tumour development resulting from the defect in DNA repair. The management of complications of XP, especially orofacial tumours entails an enormous surgical challenge to the clinicians. We present five cases of XP.