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World J Pediatr Congenit Heart Surg ; 10(5): 632-634, 2019 09.
Artigo em Inglês | MEDLINE | ID: mdl-31496409

RESUMO

Ewing sarcoma is the second most prevalent primary malignant bone tumor. Metastases from Ewing sarcoma to the heart are very rare. Herein, we present a case of undiagnosed Ewing sarcoma in a 12-year-old boy who presented with metastasis to the left atrium. The mass was prolapsing across the mitral valve. In view of the potential risk of embolization, urgent cardiac surgery was performed before the establishment of a definitive diagnosis. Histopathology was consistent with Ewing sarcoma. Subsequent magnetic resonance imaging revealed a mass in his left fibula. The patient was referred to the oncology center and received chemotherapy. One year later, he is alive with no evidence of recurrent cardiac involvement.


Assuntos
Neoplasias Ósseas/diagnóstico , Neoplasias Cardíacas/diagnóstico , Neoplasias Cardíacas/cirurgia , Sarcoma de Ewing/diagnóstico , Asma/complicações , Neoplasias Ósseas/patologia , Procedimentos Cirúrgicos Cardíacos , Criança , Embolização Terapêutica , Átrios do Coração/patologia , Neoplasias Cardíacas/secundário , Humanos , Imageamento por Ressonância Magnética , Masculino , Prolapso da Valva Mitral/patologia , Metástase Neoplásica , Sarcoma de Ewing/patologia
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