Inter-arterial course of the left coronary artery with a commissural origin in a 40-year-old patient with tricuspid atresia post Fontan shunt.

We report a case of an adult male with Tricuspid atresia post Fontan shunt in whom a rare coronary anomaly was demonstrated on Computed Tomography angiography using endoluminal views and volume rendering techniques.

Postoperative intrapulmonary invagination of the left internal mammary artery-An anomalous course deciphered on CT angiography.

We hereby present a case of intrapulmonary invagination of the left internal mammary artery detected on CT angiography. We aim to highlight the role of CT angiography in identifying these course anomalies and their clinical implications.

An unusually long intra-atrial course of the right coronary artery detected on CT angiography.

We hereby present an unusually long intra-atrial course of the right coronary artery incidentally detected on computed tomography angiography. Although usually asymptomatic, an intra-atrial right coronary artery may be injured during iatrogenic procedures which require right heart catheterisation.

Coexistence of carotid trunk and aberrant right subclavian artery originating close to left subclavian artery in tetralogy of fallot-A rare aortic arch branching anomaly.

We hereby present a patient with tetralogy of Fallot in whom a carotid trunk and aberrant right subclavian artery (arising just next to the origin of the left subclavian artery) were diagnosed on computed tomography (CT) angiography. We aim to highlight the role of CT angiography in identifying these rare aortic arch branching anomalies, which are crucial information for the operating surgeon.

Partial anomalous pulmonary venous drainage to persistent left superior caval vein: Or is it a "levoatriocardinal vein"?

We report a case of a 3-month-old girl with pulmonary atresia and intact ventricular septum where computed tomography (CT) angiography demonstrated an anomalous venous channel connecting the left brachiocephalic vein to the left atrium and all the pulmonary veins draining the left lung were seen draining individually into this channel. The case highlights the differential diagnosis of such veno-venous connections between the systemic and pulmonary venous circulations as well as the growing role of CT angiography in the understanding of these venous anomalies in the setting of complex congenital heart diseases.

Levoatriocardinal vein in a patient with transposition of great arteries and pulmonary stenosis.

We report a case of a 3-month-old boy transposition of great arteries, ventricular septal defect, and pulmonary stenosis where computed tomography (CT) angiography detected a "levoatriocardinal vein" connecting the left superior pulmonary vein and the left brachiocephalic vein with a preserved normal connection between the left superior pulmonary vein and left atrium. This case highlights the hemodynamic implications of a "levoatriocardinal vein" as well as the role of CT angiography in detecting such associated cardiovascular anomalies in patients with complex congenital heart defects.

Separate origin of left external and internal carotid arteries directly from aortic arch in a patient with double outlet right ventricle.

We report a case of a 1-year-old boy with double outlet right ventricle where computed tomography (CT) angiography incidentally demonstrated the separate origin of the left external and internal carotid arteries directly from the left-sided aortic arch with absence of a left common carotid artery. The case highlights the underlying embryological hypothesis as well as the importance of CT angiography in identifying anomalies of the aortic arch and arch vessels in the setting of complex congenital heart defects.

Evaluation of cardiovascular morphology and associated anomalies in patients with crossed pulmonary arteries on multidetector computed tomography angiography.

AIM: The present study sought to study morphology and associated cardiovascular anomalies in patients with crossed pulmonary arteries on multidetector computed tomography (CT) angiography. MATERIALS AND METHODS: We retrospectively evaluated all CT angiography studies performed at a tertiary medical center from January 2014 to December 2021 to identify patients with crossed pulmonary arteries. The associated cardiovascular anomalies as identified on CT angiography were evaluated. RESULTS: Out of 4773 patients who had undergone CT angiography for evaluation of congenital heart diseases, we identified 24 (0.5%) patients (18 males; mean age: 7.7 years) with crossed pulmonary arteries. Tetralogy of Fallot was associated in seven (29.17%) patients, double outlet right ventricle in one (4.17%) patient, and common arterial trunk in four (16.67%) patients. An aortopulmonary window was seen in three (12.5%) patients while atrial septal defect and ventricular septal defect were seen in two (8.33%) and 16 (66.67%) patients, respectively. Aortic arch anomalies were present in 16 (66.67%) patients including interrupted aortic arch and coarctation of aorta with hypoplastic aortic arch seen in two (8.33%) patients each. A double aortic arch with an atretic left arch was seen in one (4.17%) patient. Coronary artery anomalies were seen in three (12.5%) patients. CONCLUSION: Crossed pulmonary arteries are a rare anomaly and their presence suggests the coexistence of a variety of cardiovascular anomalies, including aortic arch anomalies and outflow tract malformations. Comprehensive CT angiography-based evaluation of cardiovascular morphology is imperative in the presence of crossed pulmonary arteries to facilitate presurgical planning.

Meandering Retrosternal Course of Right Coronary Artery: Partially Empty Right Atrioventricular Groove.

We report a case of a 35-year-old man with a dilated ascending aorta and a unique meandering retrosternal course of the right coronary artery (RCA) resulting in a partially empty right atrioventricular groove. The aortic root showed an exaggerated clockwise rotation, resulting in an anteriorly directed RCA ostium and the RCA, instead of entering the right atrioventricular groove, traversed caudally in the subepicardial space over the anterior surface of the right ventricle directly posterior to the sternum.

Venous vascular ring-A rare congenital venous anomaly in a patient of tetralogy of Fallot.

We hereby present a case of tetralogy of Fallot with duplicated brachiocephalic vein having a preaortic and a subaortic component. We aim to highlight the role of computed tomography angiography in identifying these rare associations of tetralogy of Fallot.

A rare case of tetralogy of Fallot-pulmonary atresia with absent right pulmonary artery and anomalous origin of left pulmonary artery from ascending aorta.

We report a case of a 5-year-old child with tetralogy of Fallot-pulmonary atresia with anomalous origin of left pulmonary artery from ascending aorta and right lung supplied by collateral arteries. This case highlights the role of preoperative CT angiography in differentiating this entity from a common arterial trunk with discontinuous pulmonary arteries.

Double aortic arch with partially atretic left arch detected on CT angiography in a case of double-chambered right ventricle: A rare association.

We report an 11-year-old child with double-chambered right ventricle detected on echocardiography in whom computed tomography (CT) angiography revealed a rare arch anomaly double aortic arch with atretic left arch. This case highlights the ability of CT angiography in identifying such cardiovascular anomalies which have clinical and surgical implications.

Imaging characteristics and associations of left atrioventricular valve atresia and patent aortic root with lateralized atrial chambers on multidetector CT.

AIM: To study the imaging characteristics and the associations of left atrioventricular valve atresia with patent aortic root and lateralized atrial chambers on multidetector computed tomography (CT) angiography. MATERIALS AND METHODS: We retrospectively evaluated all the CT angiography studies performed for the evaluation of various congenital heart diseases at our center from January 2014 to December 2021. Cases with left atrioventricular valve atresia and patent aortic root with lateralized atrial chambers were identified. The types of cardiovascular involvement as identifiable on CT angiography were studied and compiled. RESULTS: A total of 38 patients with left atrioventricular valve atresia and patent aortic root were included (median age: 5 months, males: 31). A total of 89.5% had usual atrial arrangement and 10.5% had mirror imagery of atria. Normal drainage of right and left superior caval veins and inferior caval vein into systemic venous atrium was seen in 77.8%, 61.5%, and 86.6%, respectively. Anomalous pulmonary venous drainage was seen in 3 (7.9%) patients. Atrial and ventricular septal defects were the most common associations. Imperforate left atrioventricular membrane was seen in 9 (23.7%) patients and absent left atrioventricular connection in 27 (71.1%). Discordant right atrioventricular connection was seen in 5 (13.1%) patients. While a double outlet right ventricle (76.3%) was the most common ventriculoarterial connection, discordant ventriculo-arterial connection (transposition) in 4 (10.5%). Most patients had good sized pulmonary arteries. Patent arterial duct and right aortic arch were seen in 29% and 21%, respectively. Aberrant right subclavian artery was the most common arch vessel anomaly. Coronary anomalies were seen in 7 patients (19%); single coronary artery being the most common. CONCLUSIONS: Majority of the patients with left atrioventricular valve atresia and patent aortic root with lateralized atrial chambers have usual atrial arrangement, normal right atrioventricular connections and a double outlet configuration of the right ventricle. Absent left atrioventricular connection is a more common than imperforate left atrioventricular valve membrane. Atrial and ventricular septal defects are the most common associations. Comprehensive CT based evaluation of vascular and nonvascular thoracic structures is imperative before surgery or interventions in patients with mitral atresia.

Bicuspid aortic valve and anomalous origin of the right ventricular branch in a patient with congenitally corrected transposition of great arteries: A rare association.

We hereby present a case of congenitally corrected transposition of great arteries association of bicuspid aortic valve morphology and anomalous separate origin of the right ventricular branch of the right coronary artery. We aim to highlight the role of computed tomography angiography in identifying these rare associations.

Intrathymic course of left brachiocephalic vein: A hitherto undescribed anatomical variant in tetralogy of Fallot.

We hereby present a case of a unique intrathymic course of left brachiocephalic vein in a patient with Tetralogy of Fallot and aberrant right subclavian artery deciphered on computed tomography angiography.