RESUMO
BACKGROUND: Granular cell tumors are uncommon neoplasms that can involve the skin and subcutaneous tissue. Currently, they are thought to be of neurogenic origin and most likely originate from Schwann cells. CASE PRESENTATION: This is a case of a 33-year-old woman with a growing vulvar tumor during the past year. Physical examination reveals a 2 × 1-cm mass in the lower third of the right labium majus and adjacent perineal skin. The lesion is excised, and the pathological report informs of the presence of a granular cell tumor. CONCLUSIONS: Granular cell tumors are uncommon neoplasms but should always be included as a possibility in the differential diagnosis of vulvar lesions. The treatment of choice is local wide excision, which is curative in most of the cases.
