RESUMO
An 11 day-old-girl was transferred to our hospital for surgical treatment of craniosynostosis. Either her fam- ily history or intrauterine growth was not remarkable. In addition to craniofacial deformities such as brachy- cephaly due to bicoronal craniosynostosis, high-arched palate, inferiorly positioned ears and midfacial defor- mity, she was accompanied with cardiovascular anom- alies including patent foramen ovale, patent ductus arteriosus, pulmonary artery stenosis as well as low anal atresia. She underwent general anesthesia for suture craniotomy at the age of one month. After induction of general anesthesia with sevoflurane and confirming adequate mask ventilation, fentanyl and rocuronium were administered. Direct laryngoscopy revealed Cormack-Lehane grade to be 1, followed by orotracheal intubation with a 3.5 mm uncuffed tube. A diagnosis of Saethre-Chotzen syndrome was made at the age of six months based on the result of genetic test She underwent general anesthesia for additional three times for fronto-orbital advancement, removal of the destruction devices and perineal anoplasty at 11, 15 and 16 months, respectively, which was performed uneventfully. She has no physical development disor- ders, with delay in language development at the age of 27 months.
