RESUMO
Laryngeal leiomyosarcoma is a highly infrequent malignancy, with less than fifty reports in the scientific literature world-wide. Diagnosis is based on immunohistochemistry and, occasionally, on electron microscopy techniques, making it difficult to be done preoperatively. We report a new case of laryngeal leiomyosarcoma, with an up-to-date review of the differential diagnosis and the treatment strategy.
Assuntos
Transtornos de Deglutição/etiologia , Neoplasias Laríngeas/complicações , Neoplasias Laríngeas/patologia , Leiomiossarcoma/complicações , Leiomiossarcoma/patologia , Idoso , Transtornos de Deglutição/diagnóstico , Diagnóstico Diferencial , Feminino , Humanos , Neoplasias Laríngeas/cirurgia , Leiomiossarcoma/cirurgiaRESUMO
El leiomiosarcoma laríngeo es un tumor extraordinariamente infrecuente, con menos de 50 casos descritos en la literatura mundial. Su diagnóstico implica la necesidad de técnicas de inmunohistoquímica y ocasionalmente de microscopia elestrónica, que se practica casi siempre postoperatoriamente. Presentamos un nuevo caso de leiomiosarcoma laríngeo, haciendo una revisión actualizada de su diagnóstico diferencial y de la estrategia terapéutica
Laryngeal leiomyosarcoma is a highly infrequent malignancy, with less than fifty reports in the scientific literature world-wide. Diagnosis is based on immunohistochemistry and, occasionally, on electron microscopy techniques, making it difficult to be done preoperatively. We report a new case of laryngeal leiomyosarcoma, with an up-to-date review of the differential diagnosis and the treatment strategy