RESUMO
The leiomyosarcoma of the larynx is a neoplasm extremely odd, only 46 cases are reported in the literature. We present a case seen in our Department. A male patient, 39-year-old, smoker, snoring and respiratory insufficient, who showed a whitish mass, 2.5 cm, round, steady on the right vocal fold. Urgent tracheostomy was performed but afterwards the patient refused new surgery. Biopsy revealed a malignant tumour of fusiform cells, validating as diagnostic through immunohistochemical analysis, a leiomyosarcoma case. Five months later the patient was seen again and a total laryngectomy performed. Eleven months after surgery the patient is alive and no signs of recurrence detected. In this paper diagnosis and treatment of leiomyosarcoma is discussed.
Assuntos
Neoplasias Laríngeas/patologia , Leiomiossarcoma/patologia , Adulto , Humanos , Neoplasias Laríngeas/cirurgia , Laringectomia , Leiomiossarcoma/cirurgia , MasculinoRESUMO
The cause of fibrous dysplasia of the bone is obscure. We reviewed the available literature concerning temporal bone involvement and analyzed temporal bone involvement and analyzed the most common aspects of this fascinating disease, adding three cases of our own. A clinical staging is proposed: stage 1, latent; stage 2, symptomatic; and stage 3, complication. Clinical evolution and follow-up are described and treatment is suggested.