RESUMO
Objective To discuss the high resolution CT (HRCT) characteristics of pulmonary lymphangioleiomyomatosis (PLAM),and improve the diagnosis ability of the disease.Methods The pulmonary HRCT changes in 13 patients with pathology proved PLAM were retrospectively analyzed.Results The reported 13 cases of PLAM were all female,the average onset age was 40 (28-57) years old.HRCT showed bilateral,diffuse thin walled cysts throughout both lungs in 11 cases.The cystic air spaces ranged in diameter from a few millimeter to 2 cm,the thickness of the cyst walls was 1-2 mm,air bag cavity surrounded by normal lung tissue.Multiple well-defined cystic air spaces surrounded by uniformly thin wall in 2 cases,no normal lung tissue between the air cavity.One case had complications of left side pleural effusion and lymph nodes of multiple retroperitoneal.Conclusion The HRCT findings of PLAM has diagnostic performance,and it should be used as the first choice for the diagnosis of the disease.
