Neurocitoma atípico de cerebelo que simula un hemangioblastoma. Presentación de un caso / Atypical cerebellar neurocytoma resembling a hemangioblastoma. A case report

Hasta agosto 2013 se han descrito alrededor de 105 casos de neurocitomas extraventriculares intracraneales, de los cuales el 6% se localizan en el cerebelo y el 22% son neurocitomas extraventriculares atípicos. El neurocitoma extraventricular atípico es una variante infrecuente, con solo 24 casos descritos y con un pronóstico más sombrío que el neurocitoma central típico. Se presenta un neurocitoma extraventricular atípico de cerebelo, nunca publicado hasta la fecha; de ahí el interés de este trabajo. Destaca la singularidad de ser un tumor quístico con nódulo mural, una presentación poco frecuente. Los neurocitomas extraventriculares son tumores con baja incidencia que deben considerarse en el diagnóstico diferencial inicial de lesiones cerebelosas quísticas con nódulo mural. Dado que el pronóstico depende del grado de atipia y de la resección quirúrgica, en casos de neurocitomas extraventriculares atípicos el seguimiento debe ser más estrecho, por el mayor riesgo de recidivas que presentan

Through August 2013, 105 cases of intracranial extraventricular neurocytoma (EVN) had been described; 6% were located in cerebellum and 22% were atypical EVN.A rare morphologic form of neurocytoma, atypical EVN has had only 24 cases reported to date. Its prognosis is poorer than the typical central neurocytoma. This case report describes an atypical cerebellar EVN, a form that has not been reported yet, hence the interest of this article. We emphasise its cystic nature and mural nodule, in an infrequent presentation.EVN are low-incidence tumours that we need to take into consideration when making the differential diagnosis of cystic cerebellar lesions with mural nodule. Given that the prognosis of atypical EVNs depends on the atypical nature and on the grade of resection, medical follow up has to be more constant, due to the greater degree of recurrence

[Atypical cerebellar neurocytoma resembling a hemangioblastoma. A case report]. / Neurocitoma atípico de cerebelo que simula un hemangioblastoma. Presentación de un caso.

Through August 2013, 105 cases of intracranial extraventricular neurocytoma (EVN) had been described; 6% were located in cerebellum and 22% were atypical EVN. A rare morphologic form of neurocytoma, atypical EVN has had only 24 cases reported to date. Its prognosis is poorer than the typical central neurocytoma. This case report describes an atypical cerebellar EVN, a form that has not been reported yet, hence the interest of this article. We emphasise its cystic nature and mural nodule, in an infrequent presentation. EVN are low-incidence tumours that we need to take into consideration when making the differential diagnosis of cystic cerebellar lesions with mural nodule. Given that the prognosis of atypical EVNs depends on the atypical nature and on the grade of resection, medical follow up has to be more constant, due to the greater degree of recurrence.

Meningioma de células claras lumbosacro multifocal. Presentación de un caso y revisión de la literatura / No disponible

El meningioma de células claras es una variedad infrecuente de meningioma. Se describe el caso de un meningioma espinal multifocal de células claras presente en una paciente de 20 años de edad. Clínicamente refiere lumbalgia de aproximadamente 2 años de evolución. En el estudio de resonancia magnética nuclear (RMN) se evidencia gran tumoración lumbosacra, que ocupa el canal raquídeo de L4 a S2, asociada a 2 lesiones satélites en la región lumbar. Una tumoración intra-extradural fue resecada quirúrgicamente, confirmándose el diagnóstico anatomopatológico de meningioma de células claras. Se resecan así mismo ambas lesiones satélites con idéntico diagnóstico histológico. Por tanto, en pacientes jóvenes con lesión espinal sugestiva de meningioma debe considerarse la posibilidad de que se trate de un meningioma de células claras, así como su probable origen multifocal y la probabilidad de recidivas (AU)

[Multifocal clear cell meningioma in the sacral and lumbar spine. Case report and literature review]. / Meningioma de células claras lumbosacro multifocal. Presentación de un caso y revisión de la literatura.

Clear cell meningioma is a rare morphological form of meningioma. This case report describes a very rare case of multifocal clear cell meningioma in the sacral and lumbar spine. The patient was a 20-year-old female who presented back pain. Magnetic resonance imaging (MRI) revealed a large tumour at L4 to S2 level associated with two, smaller, satellite tumours at the lumbar level. An intra-extradural tumour was surgically removed and the pathological diagnosis of clear cell meningioma was confirmed. Both satellite lesions were also resected and their histopathological diagnosis was the same. Therefore, clear cell meningioma should be considered in young patients with suggested meningioma in the lumbar spine, as well as the possibility of multifocal origin and postoperative recurrence.