RESUMO
Los mixomas intramusculares son tumores benignos y poco frecuentes, que se presentan predominantemente en los miembros inferiores. Más infrecuente es la asociación de mixomas y de displasia fibrosa, generalmente poliostótica. Esta asociación se conoce como síndrome de Mazabraud, de la que se han descrito aproximadamente 81 casos en la literatura. Presentamos un nuevo caso de esta rara asociación, para enfatizar la importancia de reconocer este síndrome en el diagnóstico y manejo adecuado del paciente (AU)
Intramuscular myxomas are benign and rare tumors that affects predominantly the lower limbs. The association of myxomas and fibrous dysplasia, usually polyostotic, is rarer. This association is known as Mazabraud's syndrome, of which about 81 cases have been described in the literature. We present a new case of this uncommon association to emphasise the importance of recognizing this syndrome in the diagnosis and appropriate management of the patient (AU)
Assuntos
Humanos , Masculino , Adulto , Displasia Fibrosa Poliostótica/complicações , Displasia Fibrosa Poliostótica/diagnóstico , Displasia Fibrosa Poliostótica/cirurgia , Mixoma/complicações , Mixoma/cirurgia , Neoplasias de Tecidos Moles/complicações , Neoplasias de Tecidos Moles/diagnóstico , Coxa da Perna/patologia , Coxa da Perna , Imageamento por Ressonância Magnética/métodos , Espectroscopia de Ressonância Magnética/métodosRESUMO
Intramuscular myxomas are benign and rare tumors that affects predominantly the lower limbs. The association of myxomas and fibrous dysplasia, usually polyostotic, is rarer. This association is known as Mazabraud's syndrome, of which about 81 cases have been described in the literature. We present a new case of this uncommon association to emphasise the importance of recognizing this syndrome in the diagnosis and appropriate management of the patient.
