RESUMO
Twisting of the spleen on its pedicle, due to the lack of the normal fixation elements, is a rare pathological condition in childhood. The revised literature reports 11 cases under the age of 10 years. We present three new cases treated at the Clínica Infantil "La Paz" (Madrid) during a period of 15 years. Ages of the three patients were 18 months, 15 months and a newborn, operated upon at 10 days. It is important to point out that only two cases of the 11 reported in the literature were younger than 12 months of age. This article also presents the embriological study of this malformation and discusses its clinic, diagnostic and treatment.
Assuntos
Esplenopatias/cirurgia , Neoplasias Abdominais/diagnóstico , Diagnóstico Diferencial , Feminino , Humanos , Lactente , Recém-Nascido , Ligamentos , Masculino , Doenças de Niemann-Pick/complicações , Esplenectomia , Esplenopatias/diagnóstico , Esplenopatias/embriologia , Anormalidade TorcionalRESUMO
This is a review of 12 cases with apple peel small bowel with agenesis of the dorsal mesentery and intestinal atresia, 11 of them jejunal and 1 duodenal in type who were treated at the Clinica Infantil "La Paz" Madrid over a period of ten years (1969--1979). The associated anomalies, the surgical treatment and the cause of death as well as the etiology and pathogenesis of this malformation are discussed.
