RESUMO
Desmoplastic fibroblastoma is a benign, rare, slow-growing soft tissue tumor which is found in a wide anatomic distribution, predominantly in adult males. The characteristic gross aspect is that of a typical cartilage-like tumor which histologically presents regular fibroblastic proliferation, often in a stellar shape within a dense collagen or myxo-collagen stroma. We report a new case observed in the foot and study the anatomic and clinical aspects of this rare entity.
Assuntos
Fibroma Desmoplásico , Doenças do Pé , Neoplasias de Tecidos Moles , Adulto , Feminino , Fibroma Desmoplásico/diagnóstico por imagem , Fibroma Desmoplásico/patologia , Fibroma Desmoplásico/cirurgia , Seguimentos , Pé/patologia , Doenças do Pé/diagnóstico , Doenças do Pé/diagnóstico por imagem , Doenças do Pé/patologia , Doenças do Pé/cirurgia , Humanos , Imuno-Histoquímica , Imageamento por Ressonância Magnética , Neoplasias de Tecidos Moles/diagnóstico por imagem , Neoplasias de Tecidos Moles/patologia , Neoplasias de Tecidos Moles/cirurgia , Fatores de Tempo , Tomografia Computadorizada por Raios XRESUMO
Sclerosing epithelioid fibrosarcoma is a rare variant of fibrosarcomas, which was recently identified as a separate entity due to specific histologic and immunohistochemistry features and its poor prognosis. We report a case of sclerosing epithelioid fibrosarcoma of soft tissues, which developed in a 37-year-old woman who presented a tumor involving the posteromedial aspect of the left knee and which progressed in size for one year. Imaging revealed a well-delimited tumor process measuring 8 cm in its largest diameter and situated in the medial compartment of the left knee. Histology of the tumorectomy specimen and the immunohistochemistry study led to the diagnosis of sclerosing epithelioid fibrosarcoma of soft tissues. This new case illustrates the characteristic features of this tumor and recalls the difficult pathological diagnosis.
