Epidural Analgesia with Ropivacaine during Labour in a Patient with a SCN5A Gene Mutation.

SCN5A gene mutations can lead to ion channel defects which can cause cardiac conduction disturbances. In the presence of specific ECG characteristics, this mutation is called Brugada syndrome. Many drugs are associated with adverse events, making anesthesia in patients with SCN5A gene mutations or Brugada syndrome challenging. In this case report, we describe a pregnant patient with this mutation who received epidural analgesia using low dose ropivacaine and sufentanil during labour.

Anaesthetic management of two patients with pompe disease for caesarean section.

The introduction of enzyme replacement therapy and the resultant stabilisation or improvement in mobility and respiratory muscle function afforded to patients with late-onset Pompe may lead to an increased number of Pompe patients prepared to accept the challenges of parenthood. In this case report, we describe our anaesthetic management of two patients with Pompe disease for a caesarean section.

Rapidly progressive laryngeal oedema associated with pregnancy-aggravated hypertension.

We report a patient with pregnancy-aggravated hypertension who developed rapid progression of laryngeal oedema intraoperatively and in whom airway obstruction occurred immediately following extubation. There were no pre-operative signs to indicate potential airway problems.