A case of portal cavernoma--associated essential thrombocythemia.

Portal cavernoma is a rare complication of portal vein thrombosis and may be a component of the myeloproliferative hematologic disorders. In the present case report, although the symptoms induced by portal hypertension and portal biliopathy had a concordant evolution with the portal cavernoma, the peripheral thrombocytosis and the medullar expression of essential thrombocythemia became relevant at 18 months.