RESUMO
Echinococcosis is a multisystem disease and has propensity to involve any organ, an unusual anatomical site, and can mimic any disease process. The hydatid cyst of the mesenteries known to occur secondary to hepatic involvement but occasional cases of his primitive form has also been reported. We report here one such case of primitive mesenteric hydatid cyst herniated through inguinal canal in a 5-yr-old boy, admitted to our Pediatric Surgery Department of Children's Hospital in Tunis, Tunisia in 2015.
RESUMO
BACKGROUND: Diaphragmatic eventration (ED) is a rare anomaly defined by a permanent elevation of a hemidiaphragm without defects. Clinical manifestations are diverse, ranging from asymptomatic to life-threatening respiratory distress. The aim of this study is to report our experience of management of eight children with ED over the past 15 years. METHODS: A retrospective study was conducted involving 8 infants and children with ED managed at the department of pediatric surgery of Tunis Children's Hospital. RESULTS: Five patients (2 males, 3 females) whose ages ranged from 5 month to 7 years (mean, 13 months) were operated on using diaphragmatic plication (3 right-sided and 2 left-sided plications) for symptomatic ED with a dramatic improvement in their respiratory status. Another infant (a 3-month-old boy) was admitted for respiratory distress that required mechanical ventilatory support. He died before operation because of sepsis. Two other asymptomatic patients with incidentally diagnosed ED were followed up for 5 years on average. Chest x-ray suggested eventration in all cases. Ultrasound was found to be a useful modality for diagnosis in 6 cases. There were no cases of associated malformation. CONCLUSION: Diaphragmatic eventration in children is usually congenital but may be acquired. Chest ultrasound is an important imaging modality for diagnosis. Diaphragmatic plication appears to be safe and effective. Surgical intervention is not recommended in asymptomatic patients.
Assuntos
Eventração Diafragmática/diagnóstico , Eventração Diafragmática/terapia , Doenças Raras/diagnóstico , Doenças Raras/terapia , Criança , Pré-Escolar , Feminino , Hospitais Pediátricos , Humanos , Lactente , Masculino , Radiografia Torácica , Estudos Retrospectivos , Tunísia/epidemiologiaAssuntos
Cistos/complicações , Doenças do Recém-Nascido/diagnóstico , Volvo Intestinal/complicações , Síndrome de Aspiração de Mecônio/complicações , Adolescente , Criança , Cistos/diagnóstico por imagem , Feminino , Humanos , Recém-Nascido , Volvo Intestinal/diagnóstico por imagem , Intestino Delgado/patologia , Síndrome de Aspiração de Mecônio/diagnóstico por imagem , Gravidez , Gravidez na Adolescência , RadiografiaAssuntos
Carcinoma de Células Pequenas/complicações , Hipercalcemia/etiologia , Neoplasias Ovarianas/complicações , Carcinoma de Células Pequenas/diagnóstico por imagem , Carcinoma de Células Pequenas/terapia , Criança , Feminino , Humanos , Hipercalcemia/diagnóstico por imagem , Hipercalcemia/terapia , Neoplasias Ovarianas/diagnóstico por imagem , Neoplasias Ovarianas/terapia , Anormalidade Torcional/complicações , Anormalidade Torcional/diagnóstico por imagem , Anormalidade Torcional/terapia , UltrassonografiaAssuntos
Extrofia Vesical/patologia , Umbigo/anormalidades , Fístula da Bexiga Urinária/patologia , Extrofia Vesical/complicações , Extrofia Vesical/cirurgia , Humanos , Recém-Nascido , Masculino , Dermatopatias/complicações , Dermatopatias/patologia , Dermatopatias/cirurgia , Umbigo/cirurgia , Fístula da Bexiga Urinária/complicações , Fístula da Bexiga Urinária/cirurgiaAssuntos
Atresia Esofágica/complicações , Estenose Pilórica Hipertrófica/complicações , Atresia Esofágica/diagnóstico por imagem , Humanos , Recém-Nascido , Doenças do Recém-Nascido/diagnóstico por imagem , Masculino , Estenose Pilórica Hipertrófica/congênito , Estenose Pilórica Hipertrófica/diagnóstico por imagem , RadiografiaRESUMO
The aim of this study was to identify the prognostic factors of intraoperative haemorrhage, perioperative blood transfusions and morbidity. We collected 120 splenectomies in Beau Séjour department of surgery, Charles' Nicolle Hospital, Tunis, Tunisia between 1979 and 1999. The descriptive analysis showed sex-ratio 0.82 with mean age (+/- standard deviation) 30.6 +/- 15 year. Idiopathic thrombopenic purpura was the principal disease indicating splenectomy. Morbidity was defined as occurrence of post operative peritoneal sepsis or bleeding. The mortality and morbidity rates were respectively 0.8% and 6.6%. The prognostic analysis didn't identify predictive factors of intraoperative haemorrhage, however it identified two independent predictive actors of specific morbidity: intraoperative haemorrhage (p = 0.03) and preoperative rate of haemoglobin (p = 0.0049).