Recurrent Abdominal Aggressive Fibromatosis with Incapacitating Hip Contracture - A Case Report.

Introduction: Aggressive fibromatosis (AF) is a fibroblastic locally aggressive neoplasm arising from the musculoaponeurotic stroma and has no metastatic potential. The high tendency of recurrence despite complete surgical resections makes the management of the condition onerous. It can result in significant morbidity with major functional loss due to the destruction of adjacent vital structures and organs. AF with hip flexion contracture is a very rare occurrence. Case Report: A 20-year-old male presented with recurrent abdominal AF with severe hip flexion contracture and an unresectable tumor. He underwent deformity correction and he maintains the full correction achieved along with very good functional improvement at the end of 4 years. Conclusion: This case demonstrates that in a case of AF with an unresectable tumor, good functional outcome can be obtained; it can be maintained over the short term following contracture release with soft-tissue coverage surgery along with chemotherapy with sorafenib.

Short-Term Outcomes of Robotic Lateral Unicompartmental Knee Arthroplasty: An Indian Perspective.

Background: Lateral UKA is a technically more challenging procedure than medial UKA accounting for < 1% of all knee arthroplasties. Robotic UKA for lateral compartment arthritis is rare and has not been reported in India. Materials and Methods: This is a prospective single-centre clinical study of six patients (five females and one male) who underwent robotic-arm-assisted lateral UKA (RALUKA) between May 2018 and January 2020 with patient-specific 3D-CT preoperative plan. Overall satisfaction on a five-level Likert scale, clinical outcome based on the KOOS and MFJS and radiological outcomes based on the HKA axis, femorotibial angle (FTA), tibial posterior slope (PS) obtained were compared preoperatively and postoperatively. Results: At a mean follow-up period of 23.84 months, among six patients 33.3% very satisfied, 50% satisfied and 16.7% felt neutral. The mean KOOS changed from 63.03 ± 3.52 to 93.95 ± 3.25 and the mean MFJS was 75.41 ± 10.29 postoperatively. The mean HKA axis changed from 175.81° ± 2.88 valgus to 179.99° ± 2.14 neutral alignment. The mean correction attained was from 4.19° ± 2.88 valgus deformity to 0.01° ± 2.14. The mean FTA and the mean PS changed from 7.34° ± 4.14 of valgus to 1.92° ± 1.85 of valgus and 83.44° ± 1.77 to 85.38° ± 2.10, respectively. Conclusions: The mean preoperative and postoperative KOOS showed a statistical significance with a p value of < 0.001 (< 0.05), showing significant improvement with RALUKA. RALUKA is a promising surgical option for lateral compartment OA of the knee.

Indian Subcontinent's First Bilateral Supracondylar Level Upper Limb Transplantation.

Introduction This is the first case of supracondylar level transplant from the Indian subcontinent, performed for a bilateral below elbow amputee. It has a completely different set of challenges for the transplant team, with a relatively shorter ischemia time window. The technical considerations for the same have been discussed in detail in this article. Materials and Methods The patient was a 19-year-old female who lost her both upper limbs at proximal forearm level due to severe crush injury following a road traffic accident. Insufficient bone length on either side necessitated a supracondylar level transplant. The preoperative workup included detailed clinical evaluation, biochemical, and psychological evaluation. The donor was a young brain-dead, male patient from a hospital, 30 minutes away. The donor and recipient preparations in this case were unique. The recipient's own elbow flexors and extensors were used while the elbow joint was from the donor. The specific challenges we faced during this procedure have been described in detail. Results The transplantation has been a complete technical success, with the patient rehabilitated back to her independent life style. This article describes only the technical considerations. The functional recovery aspect is part of an another soon to be published manuscript. Conclusion Supracondylar level arm-transplant requires a highly coordinated team effort with precise preoperative planning, along with meticulous attention to detail to achieve a successful outcome. In properly selected patients, it could be a life-changing procedure, worth all the effort.

First two bilateral hand transplantations in India (Part 2): Technical details.

INTRODUCTION: This article deals with two patients who underwent bilateral hand transplantation following amputation of both upper limbs at the distal third of the foream. MATERIALS AND METHODS: The first patient had a history of loss of hands in a train accident , with possiblity of a run over element during the injury. The second patient lost his both hands in a mine blast. The preoperative work up included detailed clinical and psychological evaluation. The donor retrieval was similar in both the cases and the donors were housed in our own instittution. The donor preparation, recipient preparation and the transplant procedure was similar except for the need of primary tendon transfers in the left hand of the first patient. RESULTS: The first patient needed a free flap transfer to cover compromised skin flap on the left hand on the second day. The second hand transplant was uneventful. Both the recipients are now back to their normal daily routines. CONCLUSIONS: Hand transplantation is a potentially life altering procedure, but to optimise the results, it is imperative that there is a meticulous planning and diligent execution with utmost importance to the detail coupled with a synchronised team effort.