[Hemihypertrophy and scoliosis revealing a Chiari 1 malformation with syringomyelia]. / Hémi-hypertrophie et scoliose révélatrices d'une malformation de Chiari de type 1 avec syringomyélie.

We report the case of a 9-year-old boy with progressive thoracic scoliosis and crossed hemihypertrophy who was discovered with a Chiari 1 malformation and syringomyelia. These disorders are connected by complex physiopathological mechanisms; their association deserves attention. This observation reviews the importance of the clinical examination, particularly the neurological exam, in childhood scoliosis. The features suggesting a neurogenic background of spine deformation should be sought. Scoliosis with hemihypertrophy can be the sign of an underlying neurological abnormality.

Congenital heart disease diagnosed in Guadeloupe.

An epidemiologic survey of congenital heart disease was performed in Guadeloupe, French West Indies, during the 3-year period 1988-1990. This survey, the first on congenital heart disease from the Caribbean, found an overall rate of 6.08 congenital heart disease cases per 1,000 live births, a high rate of hypoplastic left heart disease, and a rate of coarctation of the aorta similar to rates reported in developed countries.

PIP: Between January 1988 and December 1990 health workers referred 139 infants suspected of heart disease to a skilled pediatric cardiologist at the University Hospital of Pointe-a-Pitre, Guadeloupe. The physicians considered patent ductus arteriosus of prematurity to be a congenital heart disease if it still existed after the neonatal period. The incidence of congenital heart disease was 6.08 cases/1000 live births with a sex ratio of 1:1. 12% of chromosomal abnormalities, especially Down's syndrome. Physicians diagnosed 92% of all cases in the 1st year of life. 35% (49 infants) went to the Pediatric Cardiologic Department of Hospital Necker in Paris, France, to undergo catheterizations. 32 of these infants also underwent chest surgery. Prevalence of coarctation of the aorta (3.1/10,000 live births) essentially equalled that of developed countries. The prevalence of hypoplastic left heart disease was considerably higher than the rate in the literature (3.5/10,000 live births vs. 0.5-2.7/10,000 live births). It was the 4th ranking congenital heart disease in this population (5.7% of all cases). All the infants with hypoplastic left heart disease died.

Gongenital heart disease diagnosed in Guadeloupe

An epidemiologic survey of congenital heart disease was performed in Guadeloupe, French West Indies, during the 3-year period 1988-1990. This survey, the first on congenital heart disease from the Caribbean, found an overall rate of 6.08 congenital heart disease cases per 1 000 live births, a high rate of hypoplastic left heart disease, and a rate of coarctation of the aorta similar to rates reported in developed countries

[Leprosy in Guadeloupe 1980-1990: development and management in the general hospital]. / La lèpre en Guadeloupe 1980-1990: évolution et prise en charge a l'Hôpital général.

27 leprosy patients (19 adults, 8 children) from Basse Terre (Guadeloupe, FWI) were referred to General Hospital from 1975 to 1989: for diagnostic purpose in half the cases, for starting or modifying treatment regimens, or for complications (ENL). Lepromatous type was predominant (16/27), whereas ENL was the most serious diagnosis and therapeutic problem (7/27). Some epidemiological and psycho-social aspects are discussed.

[Infantile acropustolosis: unusual manifestation of scabies in the infant?]. / Acropustulose infantile: expression inhabituelle de la gale chez le nourrisson?

Three pediatric cases of vesiculopustules persisting for several months or years after eradication of Sarcoptes scabiei are reported. This particular course of scabies in infants is underrecognized although probably common. Its clinical manifestations, natural history and histologic features are identical to those seen in infantile acropustulosis, a recently individualized syndrome whose pathogenesis is unelucidated. In the light of these cases and a review of the literature, the possible relationship between scabies and infantile acropustulosis is discussed.

[Follow-up of HIV-I seropositive children at the Saint-Hyacinthe Hospital in Basse-Terre (Guadeloupe)]. / Suivi des enfants séro-positifs pour le VIH I à l'Hôpital Saint-Hyacinthe de Basse-Terre (Guadeloupe).

Between 1985 and 1989, we have followed twenty (20) newly born babies whose mothers were HIV seropositive. Eight of them were contaminated. Two of them died. We have studied the particular aspects of this infection in Guadeloupe.

[Marshall syndrome. 2 new cases]. / Syndrome de Marshall. Deux nouveaux cas.

Two new familial cases of Marshall syndrome are reported. The main features of this rare syndrome are outlined. Its possible relationship with Stickler syndrome is discussed.

[8 cases of diphtheria observed in Guadeloupe from 1979 to 1984]. / A propos de 8 cas de diphtérie observés en Guadeloupe de 1979 à 1984.

From 1979 to 1984, 8 cases of diphtheria were diagnosed in Basse-Terre, in children aged 11 months to 6 years. All of them were badly or not vaccinated at all. They showed the common clinical features; two patients had only pharyngitis. Corynebacterium diphtheriae was isolated from the throat in 6 patients. All children were successfully treated by early administration of antitoxin and antibiotics.

[Acute poisonings in children in Guadeloupe. 10 years' activity at a general pediatric service]. / Intoxications aiguës chez l'enfant en Guadeloupe. Dix années d'activité d'un service de pédiatrie générale.

The authors have studied all the files concerning intoxications admitted in their department throughout ten years. They stress on the epidemiologic aspects particular to this tropical country, in order to plan a program for preventing children intoxications and accidents.