1.
Hand Surg
; 12(1): 51-3, 2007.
Artigo
em Inglês
| MEDLINE
| ID: mdl-17613185
RESUMO
Maffucci syndrome belongs to a group of disorders known as enchondromatoses. First described in 1881, it features multiple enchondromas and vascular abnormalities, mainly haemangiomas. The syndrome is a variant of Ollier's disease, which consists solely of multiple enchondromas. This case serves to highlight important features of a rare condition.