1.
Ugeskr Laeger
; 183(31)2021 Aug 02.
Artigo
em Dinamarquês
| MEDLINE
| ID: mdl-34378520
RESUMO
Congenital portosystemic shunts (CPSS) are rare malformations, which connect the portal venous system and the systemic circulation. The disorder is discovered at prenatal screening, neonatal cholestasis as an incidental finding or by systemic complications such as pulmonary hypertension, encephalopathies or liver nodules. CPSS are associated to cardiac malformations and several syndromes. Intervention radiology plays a key role in treatment by closure of the shunt, which is indicated, if the patient has complications, the shunt is extrahepatic, or it is still persistent at two years of age, using a two-step approach, as summarised and discussed in this review.
Assuntos
Cardiopatias Congênitas , Hipertensão Pulmonar , Derivação Portossistêmica Transjugular Intra-Hepática , Malformações Vasculares , Criança , Feminino , Humanos , Recém-Nascido , Veia Porta/diagnóstico por imagem , Veia Porta/cirurgia , Gravidez
2.
Ugeskr Laeger
; 182(10)2020 03 02.
Artigo
em Dinamarquês
| MEDLINE
| ID: mdl-32138822