RESUMO
INTRODUCTION: Solitary Fibrous Tumor of the Pleura(SFTP) is exceedingly rare mesenchymal tumor commonly arising from the visceral pleura and accounts for <5% of all pleural tumors. Although it commonly has benign histologic characteristics, the tumor behavior is often unpredictable and less understood due to limited number of cases. CASE PRESENTATION: We present a rare case of Intrathoracic Giant SFTP in a 65 years old female who presented with a progressive worsening of shortness of breath of 1 year duration associated with intermittent dry cough, low grade fever, easy fatigability and loss of appetite. Complete enbloc resection was done and she was discharged improved. DISCUSSION: Most patients with SFTP are asymptomatic and definitive diagnosis is often made after surgical exploration and histopathologic study. Although 80% of SFTP arise from visceral pleura, the origin in our case was from the parietal pleura which is rare. CONCLUSION: SFTP should be considered as differential diagnosis in patients with atypical or recurrent respiratory symptoms despite adequate medical treatment. Complete surgical excision is the main stay of treatment and meticulous post-operative follow up is mandatory as the risk of recurrence is higher and the tumor behavior is still less understood.
RESUMO
INTRODUCTION: Bronchial carcinoid tumors are rare, slow growing, malignant neuroendocrine tumors and account for less than 2% of all lung tumors. Early diagnosis is extremely important as the main stay of treatment is surgical excision. PRESENTATION OF CASE: We present a rare case of bronchial typical carcinoid tumor in a 22-year-old female who presented with a complaint of intermittent productive cough with bloody sputum of 3 weeks' duration associated with wheezing, low grade intermittent fever and loss of appetite. She was being treated as bronchial asthma for 10 years prior to her current presentation. Right lung bi-lobectomy with regional lymph node resection was done and she was discharged home in good condition. DISCUSSION: Majority of typical carcinoids are located in the central airways leading to bronchial obstruction with recurrent pneumonia, chest pain, wheezing and hemoptysis. Due to such nonspecific presentation most patients are misdiagnosed or diagnosed late. Both typical and atypical Carcinoids have similar radiologic features and definitive diagnosis relies on bronchoscopic tissue biopsy. Although hilar and mediastinal lymph nodes are the most common metastatic sites for typical carcinoids most lymphadenopathies are caused by a reactive inflammatory reaction. CONCLUSION: Bronchial carcinoids are rare, malignant neuroendocrine tumors with complete surgical resection being the only curative management. Thus patients with recurrent respiratory symptoms despite optimum medical treatment should be thoroughly investigated for accurate and early diagnosis The outcome of typical carcinoids with lymph node metastasis is excellent with complete resection but close follow up is mandatory when dealing with larger tumors.
