RESUMO
Fourteen children with congenital hemiplegia were studied with a detailed assessment of various aspects of vision (linear acuity, stereopsis, visual fields) and MRI. The aim of this study was to evaluate the effect of a congenital lesion on visual function. The results showed a very high incidence (78%) of children who had abnormal results on at least one of the visual tests. Visual abnormalities were not correlated with the clinical severity of hemiplegia or with a specific pattern of lesion on MRI. Similarly no constant association could be found between visual structures (optic radiations and primary visual cortex) and visual function. Finally, our results would suggest that all the children with congenital hemiplegia need to be investigated irrespective of the clinical severity or of the type or the extent of the lesion. This would help to identify children with minor visual abnormalities which can affect everyday life performance.
Assuntos
Desenvolvimento Infantil/fisiologia , Hemiplegia/congênito , Hemiplegia/complicações , Imageamento por Ressonância Magnética , Transtornos da Visão/diagnóstico , Transtornos da Visão/etiologia , Adolescente , Adulto , Criança , Estudos de Coortes , Feminino , Lateralidade Funcional , Humanos , Incidência , Recém-Nascido , Itália/epidemiologia , Masculino , Estudos Retrospectivos , Transtornos da Visão/epidemiologia , Seleção Visual , Córtex Visual , Vias VisuaisRESUMO
The authors review 54 cases of diffuse bone angiomatosis (one new case and 53 from the literature) and describe the major clinical, radiological and anatomical features. The difficulties of distinguishing between haemagiomata and lymphangiomata are emphasised. The diagnosis is often helped by the presence of visceral or cutaneous lesions and when such lesions are found, a skeletal survey should always be done. These conditions, which may be classified under the general heading of angiodysplasias of bone, are hamartomata and must be distinguished from other bone lesions of vascular origin.
