RESUMO
OBJECTIVE: To report a patient with bicornuate rudimentary uterine horns with functioning endometrium and complete cervical-vaginal agenesis coexisting with ovarian endometriosis. DESIGN: Case report. SETTING: University hospital. PATIENT(S): A 37-year-old woman with an extremely rare müllerian anomaly of the uterus and vagina coexisting with ovarian endometriosis. INTERVENTION(S): Resection of the rudimentary uterine horns with bilateral salpingo-oophorectomy. MAIN OUTCOME MEASURE(S): Relief from pelvic pain after the operative procedure. RESULT(S): The definite diagnosis and removal of the müllerian anomaly and endometriosis foci. CONCLUSION(S): Cyclic pelvic pain since the age of 14 was due to cryptomenorrhoea in the presence of the bicornuate rudimentary uterine horns with functioning endometrium and cervical-vaginal agenesis. Ovarian endometriosis developed as a result. In such cases, invasive procedures, such as laparoscopy or laparotomy, should be considered to establish the diagnosis. Removing the functioning rudimentary uterine horns just after menarche should prevent the development of endometriosis and hematometra.
