RESUMO
Peliosis hepatis (PH) is a rare condition characterized by multiple blood-filled spaces within the hepatic parenchyma that can lead to fatal hemorrhage. There is no consensus on the best treatment algorithm for PH, and therapy is directed at removing the potential causative agent with operative intervention when necessary. Here we present the first known case of PH in a child with myotubular myopathy who was successfully treated with angiography and hepatic artery embolization as a first line therapy, without the need for operative intervention. Awareness of this condition and the available treatment modalities may lead to favorable outcomes in future cases.
Assuntos
Embolização Terapêutica , Doenças Genéticas Ligadas ao Cromossomo X/complicações , Artéria Hepática , Miopatias Congênitas Estruturais/complicações , Peliose Hepática/terapia , Angiografia , Criança , Emergências , Transfusão de Eritrócitos , Hemorragia/diagnóstico por imagem , Hemorragia/etiologia , Hemorragia/terapia , Artéria Hepática/diagnóstico por imagem , Humanos , Hepatopatias/diagnóstico por imagem , Hepatopatias/etiologia , Hepatopatias/terapia , Masculino , Peliose Hepática/diagnóstico por imagem , Peliose Hepática/etiologia , Plasma , Ressuscitação , Choque/etiologia , Choque/terapia , Tomografia Computadorizada por Raios XRESUMO
Mesenteric lipoma is a rare benign neoplastic condition that can grow to be very large and mimic other midgut fatty tumors. These benign tumors can cause various gastrointestinal symptoms such as obstruction and abdominal pain. We report the case of a 9-year-old boy who presented with a small bowel obstruction caused by torsion of a large mesenteric lipoma. This is an important but unusual tumor and should be considered in the differential of fatty lesions within the mesentery.
