RESUMO
The development of a second haematological disease during the course of systemic mastocytosis is a well-known phenomenon. In most of the cases, they consist of myelodysplasia or myeloproliferative disorders. The association with lymphoproliferative disorders has also been described, but it is uncommon and the relationship is not well established. We report a patient diagnosed with systemic mastocytosis who three years later developed a splenic marginal zone lymphoma with villous lymphocytes.
Assuntos
Hipopigmentação/patologia , Adolescente , Adulto , Progressão da Doença , Feminino , Humanos , Adulto JovemAssuntos
Desfibriladores Implantáveis/efeitos adversos , Eritema/etiologia , Complicações Pós-Operatórias/etiologia , Telangiectasia/etiologia , Idoso , Aneurisma da Aorta Abdominal/complicações , Aneurisma da Aorta Abdominal/cirurgia , Berílio/efeitos adversos , Eritema/patologia , Humanos , Masculino , Complicações Pós-Operatórias/patologia , Remissão Espontânea , Taquicardia Ventricular/complicações , Taquicardia Ventricular/cirurgia , Telangiectasia/patologia , Timerosal/efeitos adversosAssuntos
Braço , Neoplasias das Glândulas Sudoríparas/patologia , Idoso , Feminino , Humanos , Fatores de TempoRESUMO
Acroangiodermatitis or pseudo-Kaposi sarcoma is an angioproliferative, self-limited entity that includes a group of diseases, congenital or acquired, with cutaneous lesions similar to Kaposi sarcoma (KS). This term can lead to confusion because it comprises several entities that are completely different, nonetheless, it has an important clinical value as it guides the diagnosis and management of these patients. We report the case of a 67-year-old patient with lesions of acroangiodermatitis in both forearms secondary to arteriovenous shunts from hemodialysis. Doppler ultrasound showed a former arteriovenous fistula in addition to the one already known. Immunohistochemical study showed CD34+ staining in endotelial cells and absence of HHV-8 expression.
