Vulvar rhabdomyosarcoma in a 15-year-old girl (case report).

Knowledge of vulvar rhabdomyosarcoma (RMS) is based on case reports and collective reviews since the pathology is extremely rare and experience of individual institutions limited. We present a case of a 15-year-old girl with large-sized vulvar embryonal RMS. The patient was treated with wide local excision of the tumor, multiagent chemotherapy and radiotherapy, achieved complete remission but 6 months after diagnosis died of toxicity. The management is discussed. Necessity of early anticipation of malignancy in girls is pointed out as it may determine outcome of therapy.